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一名患有具有挑战性的巨大枕部脑膨出的日本裔男性儿童。

Challenging, giant occipital encephalocele in a pediatric saipanese male.

作者信息

Loya Joshua, Brown Nolan J, Gonda David, Levy Michael

机构信息

Department of Neurosurgery University of California San Diego, Rady's Children's Hospital San Diego California USA.

出版信息

Clin Case Rep. 2023 May 18;11(5):e7380. doi: 10.1002/ccr3.7380. eCollection 2023 May.

DOI:10.1002/ccr3.7380
PMID:37215965
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10196437/
Abstract

KEY CLINICAL MESSAGE

Giant occipital encephalocele is a rare form of congenital anomaly that involves protrusion of brain tissue (greater in size than the patient's cranial cavity) from a defect in the skull. This case reports illustrates repair of a giant encephalocele and emphasizes important methods to reduce risk for blood loss and other complications.

ABSTRACT

A rare form of congenital anomaly, giant occipital encephalocele involves protrusion of brain tissue from a defect in the skull (in this case from the occiput). While encephalocele itself is a fairly rare entity, those qualifying as "giant"-defined by size of the deformity exceeding that of the skull itself - require very technically challenging surgery.

摘要

关键临床信息

巨大枕部脑膨出是一种罕见的先天性异常形式,涉及脑组织(体积大于患者颅腔)从颅骨缺损处突出。本病例报告阐述了巨大脑膨出的修复,并强调了减少失血和其他并发症风险的重要方法。

摘要

巨大枕部脑膨出是一种罕见的先天性异常形式,涉及脑组织从颅骨缺损处(在本病例中为枕部)突出。虽然脑膨出本身是一种相当罕见的病症,但那些被定义为“巨大”的脑膨出——根据畸形大小超过颅骨本身来界定——需要极具技术挑战性的手术。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8889/10196437/a050600a8ee6/CCR3-11-e7380-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8889/10196437/534141b569e1/CCR3-11-e7380-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8889/10196437/df534a98047c/CCR3-11-e7380-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8889/10196437/2cab6ad38a16/CCR3-11-e7380-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8889/10196437/d1a5811b58e7/CCR3-11-e7380-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8889/10196437/a050600a8ee6/CCR3-11-e7380-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8889/10196437/534141b569e1/CCR3-11-e7380-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8889/10196437/df534a98047c/CCR3-11-e7380-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8889/10196437/2cab6ad38a16/CCR3-11-e7380-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8889/10196437/d1a5811b58e7/CCR3-11-e7380-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8889/10196437/a050600a8ee6/CCR3-11-e7380-g005.jpg

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A rare case of occipital encephalocele presenting as the largest congenital head mass in an infant.一例罕见的枕部脑膨出病例,表现为婴儿最大的先天性头部肿块。
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本文引用的文献

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A Brief Review of Giant Occipital Encephalocele.巨大枕部脑膨出的简要综述
J Neurosci Rural Pract. 2018 Oct-Dec;9(4):455-456. doi: 10.4103/jnrp.jnrp_189_18.
2
Perioperative Management of Children With Giant Encephalocele: A Clinical Report of 29 Cases.巨大脑膨出患儿的围手术期管理:29例临床报告
J Neurosurg Anesthesiol. 2017 Jul;29(3):322-329. doi: 10.1097/ANA.0000000000000282.
3
Giant encephalocele: a study of 14 patients.巨大型脑膨出:14例患者的研究
Pediatr Neurosurg. 2011;47(6):406-11. doi: 10.1159/000338895. Epub 2012 Jul 7.
4
Perioperative challenges in patients with giant occipital encephalocele with microcephaly and micrognathia.患有巨大枕部脑膨出合并小头畸形和小颌畸形患者的围手术期挑战。
J Neurosci Rural Pract. 2012 Jan;3(1):68-70. doi: 10.4103/0976-3147.91949.
5
Expansile cranioplasty for massive occipital encephalocele.扩张性颅骨成形术治疗巨大枕部脑膨出
Childs Nerv Syst. 2006 Sep;22(9):1170-6. doi: 10.1007/s00381-006-0110-y. Epub 2006 May 18.
6
Giant occipital encephalocele with microcephaly and micrognathia.巨大枕部脑膨出伴小头畸形和小颌畸形。
Pediatr Neurosurg. 2004 Jul-Aug;40(4):205-6. doi: 10.1159/000081941.
7
Surgical closure and reconstruction of a large occipital encephalocele without parenchymal excision.大型枕部脑膨出的手术闭合与重建,不进行实质切除。
Childs Nerv Syst. 2005 Feb;21(2):144-7. doi: 10.1007/s00381-004-1020-5. Epub 2004 Sep 4.