Lee Heng-Tien Aaron, Abosheaishaa Hazem, Nassar Mahmoud, Saliaj Merjona
Internal Medicine, St. George's University School of Medicine, True Blue, GRD.
Internal Medicine, Icahn School of Medicine at Mount Sinai, Queens Hospital Center, New York, USA.
Cureus. 2023 Apr 20;15(4):e37909. doi: 10.7759/cureus.37909. eCollection 2023 Apr.
Moyamoya disease is a rare cerebrovascular disorder characterized by progressive stenosis and occlusion of the intracranial arteries, resulting in the formation of collateral vessels. We present a case of a 24-year-old South Asian female with no prior medical history who presented with persistent headaches, right-hand numbness and pain, and global aphasia. Imaging revealed severe steno-occlusive disease involving the left internal carotid artery terminus, the proximal middle cerebral artery (MCA), and the anterior cerebral artery. The patient underwent a hemicraniectomy due to malignant MCA syndrome and was prescribed aspirin and fluoxetine. Further evaluation with a cerebral angiogram revealed severe steno-occlusive disease involving the left internal carotid artery terminus, the proximal middle cerebral artery, and the anterior cerebral artery. The patient had Moyamoya disease. This case emphasizes the necessity of including Moyamoya disease in the differential diagnosis, as it can result in serious neurological impairments.
烟雾病是一种罕见的脑血管疾病，其特征为颅内动脉进行性狭窄和闭塞，导致侧支血管形成。我们报告一例24岁的南亚女性病例，该患者既往无病史，出现持续性头痛、右手麻木和疼痛以及完全性失语。影像学检查显示严重的狭窄闭塞性疾病累及左颈内动脉末端、大脑中动脉近端和大脑前动脉。该患者因恶性大脑中动脉综合征接受了颅骨切除术，并服用了阿司匹林和氟西汀。进一步的脑血管造影评估显示严重的狭窄闭塞性疾病累及左颈内动脉末端、大脑中动脉近端和大脑前动脉。该患者患有烟雾病。该病例强调了在鉴别诊断中纳入烟雾病的必要性，因为它可能导致严重的神经功能损害。
