VEXAS综合征：一种成人起病的单基因自身炎症性疾病，尚有许多未解之谜。 - Suppr

VEXAS syndrome: an adult-onset monogenic autoinflammatory disease with many unanswered questions.

作者信息

Hernández-Rodríguez José, Nieścieruk Jakub, Maślińska Maria

机构信息

Clinical Unit of Autoinflammatory Diseases and Vasculitis Research Unit, Department of Autoimmune Diseases, Hospital Clínic of Barcelona, Spain.

Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), University of Barcelona, Barcelona, Spain.

出版信息

Reumatologia. 2023;61(2):83-85. doi: 10.5114/reum/165994. Epub 2023 May 10.

DOI:10.5114/reum/165994

PMID:37223367

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10201377/

Abstract

摘要

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ca4/10201377/663636b261ad/RU-61-165994-g001.jpg

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Ruxolitinib is more effective than other JAK inhibitors to treat VEXAS syndrome: a retrospective multicenter study.

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VEXAS syndrome: an adult-onset monogenic autoinflammatory disease with many unanswered questions.

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