Aihole Jayalaxmi Shripati
Dept of Paediatric surgery, Indira Gandhi Institute of Child Health, Bangalore, Karnataka, India.
Int J Surg Case Rep. 2023 Jun;107:108335. doi: 10.1016/j.ijscr.2023.108335. Epub 2023 May 20.
Ganglioneuromas (GNs) are hamartomatous tumors that originate in sympathetic ganglia and adrenal glands. Rarely, they might originate in enteric nervous system affecting its motility. Clinically they present with varying symptoms of pain abdomen, constipation and bleeding. Nevertheless, patients can remain asymptomatic for many years.
Author is reporting here a case of ganglioneuromatosis of intestine in a child and its effective management by a simple surgical procedure, yielding good result without morbidity.
Intestinal ganglioneuromatosis is a rare form of benign neurogenic tumor characterized by hyperplasia of ganglion cell nerve fibers and supporting cells.
Intestinal ganglioneuromatosis, diagnosed only after histopathological examination, should be managed either by conservative or surgical procedure, depending upon the clinical scenario by attending paediatric surgeon.
神经节神经瘤（GNs）是起源于交感神经节和肾上腺的错构瘤性肿瘤。它们很少起源于影响其运动的肠神经系统。临床上，它们表现为腹痛、便秘和出血等不同症状。然而，患者可能多年无症状。
作者在此报告一例儿童肠道神经节神经瘤病病例，以及通过简单手术程序对其进行的有效治疗，取得了良好效果且无并发症。
肠道神经节神经瘤病是一种罕见的良性神经源性肿瘤，其特征是神经节细胞神经纤维和支持细胞增生。
肠道神经节神经瘤病只有在组织病理学检查后才能确诊，应由小儿外科医生根据临床情况采用保守或手术方法进行治疗。
