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模仿肉芽肿性多血管炎的外周T细胞淋巴瘤。

Peripheral T-cell lymphoma mimicking granulomatosis with polyangiitis.

作者信息

Ediboğlu Elif Durak, Solmaz Dilek, Özkal Sermin, Erdoğan Nezahat Karaca, Akar Servet

机构信息

Hatay Research and Training Hospital, Hatay, Turkey.

Department of Internal Medicine, Division of Rheumatology, Izmir Katip Celebi University, Izmir, Turkey.

出版信息

Z Rheumatol. 2023 Oct;82(8):692-695. doi: 10.1007/s00393-023-01370-1. Epub 2023 May 26.

DOI:10.1007/s00393-023-01370-1
PMID:37237152
Abstract

Upper respiratory tract involvement is common in patients with granulomatosis with polyangiitis (GPA), but malignancies should be kept in mind in the differential diagnosis. A 68-year-old man was referred to rheumatology to investigate for GPA after nasal excisional biopsy. After careful radiologic and pathologic assessment, he was diagnosed with peripheral T‑cell lymphoma, nasal type. This is a rare case of T‑cell lymphoma in a patient who was referred as GPA.

摘要

上呼吸道受累在显微镜下多血管炎(GPA)患者中很常见,但在鉴别诊断时应考虑到恶性肿瘤。一名68岁男性在鼻腔切除活检后被转诊至风湿病科以排查GPA。经过仔细的影像学和病理学评估,他被诊断为鼻型外周T细胞淋巴瘤。这是一例罕见的在被诊断为GPA的患者中发生的T细胞淋巴瘤病例。

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本文引用的文献

1
[Extranodal NK-T-cell lymphoma, nasal type in granulomatosis with polyangiitis. A case report].[鼻型结外NK-T细胞淋巴瘤合并肉芽肿性多血管炎。1例报告]
Rev Med Inst Mex Seguro Soc. 2017 May-Jun;55(3):394-398.
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Natural killer/T-cell lymphoma, nasal type, masquerading as recalcitrant periodontitis in a patient with a diagnosis of Wegener's granulomatosis.NK/T 细胞淋巴瘤,鼻型,在一位韦格纳肉芽肿病诊断患者中表现为难治性牙周炎。
Am J Med Sci. 2013 Feb;345(2):163-7. doi: 10.1097/MAJ.0b013e318268bc65.
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Structured clinical assessment of the ear, nose and throat in patients with granulomatosis with polyangiitis (Wegener's).
韦格纳肉芽肿病(Wegener's)患者的耳部、鼻部和喉部的结构性临床评估。
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Arthritis Rheum. 2003 Aug;48(8):2299-309. doi: 10.1002/art.11075.
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Wegener's granulomatosis--a review of diagnosis and treatment in 53 subjects.韦格纳肉芽肿病——53例患者的诊断与治疗综述
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Head and neck involvement in Wegener's granulomatosis (WG).韦格纳肉芽肿病(WG)中的头颈部受累情况。
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