Dept. of Oral and Maxillofacial Surgery, Stomatological Hospital, China Medical University, Shenyang 110000, China.
Hua Xi Kou Qiang Yi Xue Za Zhi. 2023 Jun 1;41(3):361-364. doi: 10.7518/hxkq.2023.2022402.
Malignant peripheral nerve sheath tumor (MPNST) is a rare neurogenic malignant tumor. MPNST has aty-pical clinical symptoms and imaging presentations, difficult diagnosis, a high degree of malignancy, and poor prognosis. It usually occurs in the trunk, approximately 20% in the head and neck, and rarely in the mouth. This paper reports a case of MPNST of the tongue. A summary of the clinical features, diagnosis, and treatment of MPNST is presented in combination with a literature review to provide a reference for the diagnosis and treatment of this disease.
恶性外周神经鞘瘤(MPNST)是一种罕见的神经源性恶性肿瘤。MPNST 具有非典型的临床症状和影像学表现,诊断困难,恶性程度高,预后差。它通常发生在躯干,约 20%发生在头颈部,很少发生在口腔。本文报告了一例舌部 MPNST。结合文献复习,总结 MPNST 的临床特点、诊断和治疗,为该病的诊断和治疗提供参考。