Amin Adina, Bailey Nadian, Warren Amanda, Reddy Bharath
Internal Medicine, NewYork-Presbyterian Brooklyn Methodist Hospital, Brooklyn, USA.
Cardiac Electrophysiology, NewYork-Presbyterian Brooklyn Methodist Hospital, Brooklyn, USA.
Cureus. 2023 May 6;15(5):e38620. doi: 10.7759/cureus.38620. eCollection 2023 May.
Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a rare disorder with familial (autosomal dominant) predisposition and can be challenging to diagnose. Non-sustained ventricular tachycardia (NSVT) is a relatively uncommon and short-lived arrhythmia when seen in the general, healthy population. NSVT with a left bundle branch block morphology is usually idiopathic but may also be seen in ARVC. It can also be associated with poorer prognosis and increased mortality. Repetitive monomorphic ventricular ectopic beats may suggest ARVC, but could also be idiopathic. Timely diagnosis is vital due to the unpredictability and progressive nature of ARVC. We present a case of a 40-year-old Caucasian female with heart palpitations and NSVT found on an outpatient Holter monitor, and later found to have clinical and radiological features consistent with ARVC.
致心律失常性右室心肌病(ARVC)是一种罕见的具有家族性(常染色体显性)倾向的疾病,诊断可能具有挑战性。非持续性室性心动过速(NSVT)在普通健康人群中相对不常见且持续时间较短。具有左束支传导阻滞形态的NSVT通常为特发性,但也可见于ARVC。它还可能与较差的预后和死亡率增加有关。重复性单形性室性早搏可能提示ARVC,但也可能是特发性的。由于ARVC的不可预测性和进行性,及时诊断至关重要。我们报告一例40岁的白种女性病例,该患者因心悸在门诊动态心电图监测中发现NSVT,后来发现其临床和影像学特征与ARVC一致。