Peretz Cheryl A C, Kennedy Vanessa E, Walia Anushka, Delley Cyrille L, Koh Andrew, Tran Elaine, Clark Iain C, Hayford Corey E, D'Amato Chris, Xue Yi, Fontanez Kristina M, Roy Ritu, Logan Aaron C, Perl Alexander E, Abate Adam, Olshen Adam, Smith Catherine C
Divison of Hematology and Oncology, Department of Pediatrics, USA.
Helen Diller Family Comprehensive Cancer Center, University of California San Francisco, San Francisco, CA.
bioRxiv. 2023 May 18:2023.05.15.540305. doi: 10.1101/2023.05.15.540305.
Mixed phenotype acute leukemia (MPAL) is a leukemia whose biologic drivers are poorly understood, therapeutic strategy remains unclear, and prognosis is poor. We performed multiomic single cell (SC) profiling of 14 newly diagnosed adult MPAL patients to characterize the immunophenotypic, genetic, and transcriptional landscapes of MPAL. We show that neither genetic profile nor transcriptome reliably correlate with specific MPAL immunophenotypes. However, progressive acquisition of mutations is associated with increased expression of immunophenotypic markers of immaturity. Using SC transcriptional profiling, we find that MPAL blasts express a stem cell-like transcriptional profile distinct from other acute leukemias and indicative of high differentiation potential. Further, patients with the highest differentiation potential demonstrated inferior survival in our dataset. A gene set score, MPAL95, derived from genes highly enriched in this cohort, is applicable to bulk RNA sequencing data and was predictive of survival in an independent patient cohort, suggesting utility for clinical risk stratification.
混合表型急性白血病(MPAL)是一种生物学驱动因素尚不明确、治疗策略仍不清晰且预后较差的白血病。我们对14例新诊断的成年MPAL患者进行了多组学单细胞(SC)分析,以描绘MPAL的免疫表型、基因和转录图谱。我们发现,基因图谱和转录组均与特定的MPAL免疫表型无可靠关联。然而,突变的逐步获得与不成熟免疫表型标志物的表达增加相关。通过SC转录分析,我们发现MPAL原始细胞表达一种不同于其他急性白血病的干细胞样转录图谱,提示具有高分化潜能。此外,在我们的数据集中,具有最高分化潜能的患者生存较差。从该队列中高度富集的基因衍生出的基因集评分MPAL95,适用于批量RNA测序数据,并可预测独立患者队列的生存情况,提示其在临床风险分层中的应用价值。