Sertoli-Leydig cell tumor associated with a germline pathogenic variant diagnosed during pregnancy: Considerations for treatment, surveillance, and prevention.

•This is the first report of a germline -associated Sertoli-Leydig cell tumor (SLCT) diagnosed in pregnancy.•SLCT is linked to pathogenic variants, but little is known about management of -associated SLCT.•There is an extended risk for metachronous SLCT in patients with germline pathogenic variants who retain an ovary.•Prophylactic contralateral salpingo-oophorectomy may be offered with shared decision making to patients with inherited SLCT.•Genetic testing for should be offered to all patients with moderately or poorly differentiated SLCT.