Uzuka Takeshi, Umeta Riko, Uchiyama Hiroki, Arihara Ayaka, Hashiguchi Hitoki, Sasaki Akihiko
Cardiovascular Surgery, Sunagawa City Medical Center, Sunagawa, Hokkaido, Japan.
Ann Vasc Dis. 2023 Jun 25;16(2):139-141. doi: 10.3400/avd.cr.23-00007.
Vascular involvement, especially in the iliofemoral segment, is rare in type 1 neurofibromatosis. We herein report a case involving a 49-year-old male diagnosed with type 1 neurofibromatosis who presented with right inguinal pain and swelling. CT angiography revealed a 50-mm aneurysm extending from the right external artery to the common femoral artery. Although surgical reconstruction was performed successfully, the patient required an additional operation 6 years later for aneurysm enlargement in the deep femoral artery. Histopathological examination confirmed the proliferation of neurofibromatosis cells in the aneurysm wall.
血管受累，尤其是在髂股段，在1型神经纤维瘤病中较为罕见。我们在此报告一例病例，患者为一名49岁男性，诊断为1型神经纤维瘤病，表现为右腹股沟疼痛和肿胀。CT血管造影显示一个50毫米的动脉瘤，从右外动脉延伸至股总动脉。尽管手术重建成功，但患者在6年后因股深动脉动脉瘤增大而需要再次手术。组织病理学检查证实动脉瘤壁中有神经纤维瘤病细胞增殖。
