Department of General Surgery, Aster Sanad Hospital, Riyadh, Saudi Arabia.
Department of Basic Sciences, Sulaiman Al Rajhi Colleges, PO Box 777, Al Bukayriyah, 51941, Saudi Arabia.
J Med Case Rep. 2023 Jun 30;17(1):298. doi: 10.1186/s13256-023-03929-7.
Peliosis is a rare condition with anatomopathological characteristics that affect the liver. However, splenic peliosis is even more unique and rare. Patients with such abnormality usually exhibit no symptoms. Moreover, this is a lethal condition due to the high probability of splenic rupture accompanied by shock.
We present a case of a 29-year-old Arab female who was admitted to the hospital with severe upper abdominal pain that started 1 week from the date of admission, associated with nausea, anorexia, low-grade fever, and vomiting, with no past medical history or comorbidities. A computerized tomography scan with contrast showed intraperitoneal free fluid along with multiple hypodense splenic cysts. Hence, an emergent exploratory laparotomy with splenectomy was performed. Splenic peliosis was confirmed by the histopathological examination.
Further investigations are warranted if peliosis is confirmed in one organ, for example, the liver, to detect its presence in any other potential organs that can be affected by peliosis. Splenic peliosis is extraordinarily rare. Furthermore, such a disease has no established management plan. Definitive treatment is surgical. Many aspects of splenic peliosis remain puzzling requiring more research in the near future.
肝血管瘤病是一种具有影响肝脏的解剖病理学特征的罕见病症。然而，脾血管瘤病则更为独特和罕见。患有此类异常的患者通常没有症状。此外，由于脾脏破裂伴休克的可能性很高，这种病症是致命的。
我们介绍了一位 29 岁的阿拉伯女性，她因入院后 1 周出现严重的上腹痛、恶心、食欲不振、低热和呕吐而入院，无既往病史或合并症。腹部计算机断层扫描（CT）显示腹腔内有游离液，伴有多个脾脏低密度囊肿。因此，进行了紧急剖腹探查术和脾切除术。组织病理学检查证实为脾血管瘤病。
如果在一个器官（例如肝脏）中确诊了血管瘤病，应进一步调查以确定其在任何其他可能受血管瘤病影响的潜在器官中的存在情况。脾血管瘤病极为罕见。此外，这种疾病尚无既定的管理方案。明确的治疗方法是手术。脾血管瘤病的许多方面仍令人费解，需要在不久的将来进行更多的研究。
