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部分性房室间隔缺损伴左房室瓣瘤样扩张,酷似瓣叶穿孔。

Partial Atrioventricular Septal Defect with Left Atrioventricular Valve Aneurysm Mimicking Valve Perforation.

机构信息

Department of Cardiac Surgery, Hôpital de la Timone, Assistance Publique des Hôpitaux de Marseille, Marseille, France.

Department of Cardiology, Centre Hospitalier Universitaire Tambohobe Fianarantsoa, Antananarivo, Madagascar.

出版信息

Braz J Cardiovasc Surg. 2023 Jul 4;38(4):e20220218. doi: 10.21470/1678-9741-2022-0218.

DOI:10.21470/1678-9741-2022-0218
PMID:37402240
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10358313/
Abstract

Left atrioventricular valve aneurysm is a rare condition. Here we present a rare case of partial atrioventricular septal defect with an extremely thin left atrioventricular valve aneurysm mimicking valve perforation. Preoperative echocardiography demonstrated severe left sided atrioventricular valve regurgitation on the "cleft" and leaflet perforation. But we discovered a left sided atrioventricular valve aneurysm instead of a valve perforation. The "cleft" edge and the aneurysm were closed.

摘要

左房室瓣动脉瘤是一种罕见的情况。在此,我们报告一例罕见的部分房室隔缺损合并极薄的左房室瓣动脉瘤,其表现类似于瓣叶穿孔。术前超声心动图显示“裂隙”和瓣叶穿孔处有严重的左房室瓣反流。但我们发现的是左房室瓣动脉瘤而不是瓣叶穿孔。“裂隙”边缘和动脉瘤被封闭。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/15b5/10358313/b10aefd14a6e/bjcvs-38-04-e20220218-g04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/15b5/10358313/b74bd461dcc6/bjcvs-38-04-e20220218-g01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/15b5/10358313/e267e2fb95e2/bjcvs-38-04-e20220218-g03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/15b5/10358313/390f448385fe/bjcvs-38-04-e20220218-g02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/15b5/10358313/b10aefd14a6e/bjcvs-38-04-e20220218-g04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/15b5/10358313/b74bd461dcc6/bjcvs-38-04-e20220218-g01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/15b5/10358313/e267e2fb95e2/bjcvs-38-04-e20220218-g03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/15b5/10358313/390f448385fe/bjcvs-38-04-e20220218-g02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/15b5/10358313/b10aefd14a6e/bjcvs-38-04-e20220218-g04.jpg

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