Department of Internal Medicine, Hospital Vila da Serra, Nova Lima, Minas Gerais, Brazil.
Department of Internal Medicine, Universidade Federal de Minas Gerais, Belo Horizonte, Minas Gerais, Brazil.
Braz J Cardiovasc Surg. 2023 Jul 4;38(4):e20220320. doi: 10.21470/1678-9741-2022-0320.
Idiopathic pulmonary arterial hypertension is a rare and progressive disease with poor prognosis. Many patients progressively worsen even when using combinations of specific drugs for its treatment. Herein, we present our experience in the management of three children with severe pulmonary arterial hypertension refractory to clinical treatment who underwent Potts surgery in addition to clinical treatment.
特发性肺动脉高压是一种罕见且进行性的疾病,预后不良。许多患者即使使用特定药物联合治疗,病情也会逐渐恶化。在此,我们介绍了我们对 3 例临床治疗无效的严重肺动脉高压儿童进行 Potts 手术联合临床治疗的经验。