Yani Ahmad, Ulima Rhea Putri, Rinaldhy Kshetra, Rahayatri Tri Hening, Amaliah Rizky, Ayudyasari Wulan
Division of Pediatric Surgery, Department of Surgery, Faculty of Medicine, Universitas Indonesia, Cipto Mangunkusumo Hospital, Jakarta, Indonesia.
Department of Surgery, RSUPN Dr. Cipto Mangunkusumo, Jakarta, Indonesia.
Int J Surg Case Rep. 2023 Jul;108:108391. doi: 10.1016/j.ijscr.2023.108391. Epub 2023 Jun 9.
Giant cystic lymphangioma was a congenital lymphatic system malformation. Although it is benign, it can cause some complications requiring prompt treatment. The selection of therapy was challenging because none of them is perfect. In this report, we presented a case of multiple giant cystic lymphangiomas in an infant treated with stepwise surgeries combined with intralesional bleomycin injection.
A two-day-old infant presented with multiple, soft, skin-colored tumors on the right side of the neck, thoracoabdominal region, axilla, and upper extremity which on pre-natal MRI appeared as heterogeneous masses with septate cystic components infiltrating upper chest cavity and compressing subclavian and carotid arteries. The patient was treated successfully with stepwise surgeries followed by intralesional bleomycin injections.
Cystic lymphangioma is a benign malformation of lymphatic vessels with the neck and axillar region being the most common site. There are several options for treatment modalities. Surgery has been the mainstay of treatment, but other treatment modes are getting more popular. A combination of surgery and sclerotherapy has shown satisfying results.
In large and infiltrative lymphangioma cases, staged surgery followed by intralesional bleomycin injection can be a treatment approach to minimize morbidity and mortality.
巨大囊性淋巴管瘤是一种先天性淋巴系统畸形。尽管它是良性的，但可引发一些需要及时治疗的并发症。治疗方法的选择颇具挑战性，因为没有一种方法是完美的。在本报告中，我们介绍了一例婴儿多发性巨大囊性淋巴管瘤的病例，该病例采用了逐步手术联合瘤内注射博来霉素进行治疗。
一名两天大的婴儿在颈部右侧、胸腹区域、腋窝和上肢出现多个柔软的肤色肿瘤，产前磁共振成像显示为异质性肿块，有分隔的囊性成分，侵入上胸腔并压迫锁骨下动脉和颈动脉。该患者通过逐步手术，随后进行瘤内注射博来霉素，成功治愈。
囊性淋巴管瘤是淋巴管的一种良性畸形，颈部和腋窝区域是最常见的部位。治疗方式有多种选择。手术一直是主要的治疗方法，但其他治疗方式也越来越受欢迎。手术与硬化疗法相结合已显示出令人满意的效果。
在巨大且浸润性淋巴管瘤病例中，分期手术随后瘤内注射博来霉素可作为一种治疗方法，以尽量降低发病率和死亡率。
