Nguyen Katrin, Korsing Sören, Mansour Yasmine, Meier Katharina
Klinik für Dermatologie, Allergologie und Venerologie, Charité - Universitätsmedizin Berlin, Charitéplatz 1, 10117, Berlin, Deutschland.
Dermatologie (Heidelb). 2023 Oct;74(10):787-792. doi: 10.1007/s00105-023-05192-9. Epub 2023 Jul 5.
Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a rare hematological malignancy that derives from precursors of plasmacytoid dendritic cells and is characterized by disseminated, erythematous or bluish-livid plaques or nodi. Because of the disease's rarity the diagnosis and treatment still pose a significant challenge. We present a case of a patient with BPDCN and show clinical and diagnostic characteristics as well as potential treatment regimes.
母细胞性浆细胞样树突状细胞肿瘤(BPDCN)是一种罕见的血液系统恶性肿瘤,起源于浆细胞样树突状细胞前体,其特征为散在分布的红斑或青紫色斑块或结节。由于该疾病罕见,其诊断和治疗仍然面临重大挑战。我们报告一例BPDCN患者的病例,并展示其临床和诊断特征以及潜在的治疗方案。