From the Department of Anesthesiology, McGovern Medical School, UTHouston, Houston, Texas.
A A Pract. 2023 Jul 5;17(7):e01690. doi: 10.1213/XAA.0000000000001690. eCollection 2023 Jul 1.
Anesthetic considerations for adults with Bannayan-Riley-Ruvalcaba syndrome, part of the PTEN (phosphatase and tensin homolog) hamartoma tumor syndrome, are not well described. As patients may require surgical intervention for associated musculoskeletal, intestinal, oncologic, or soft tissue masses, knowledge of implications of anesthesia is necessary. Airway management may be challenging given macrocephaly and accumulation of lymphangiomatous tissue in the oro/hypopharynx. This report describes a patient with typical features, nonreassuring external airway anatomy, and developmental delay, which precluded an awake airway management technique. The airway was secured with the use of high-flow nasal oxygen and videolaryngoscopy.
对于患有 Bannayan-Riley-Ruvalcaba 综合征（PTEN（磷酸酶和张力蛋白同源物）错构瘤肿瘤综合征的一部分）的成年人，其麻醉考虑因素并未得到很好的描述。由于患者可能需要接受与肌肉骨骼、肠道、肿瘤或软组织肿块相关的手术干预，因此需要了解麻醉的影响。由于巨颅症和口咽/下咽淋巴管瘤组织的积聚，气道管理可能具有挑战性。本报告描述了一名具有典型特征、气道外部解剖结构不令人放心和发育迟缓的患者，这使得无法采用清醒气道管理技术。气道通过使用高流量鼻氧和视频喉镜来固定。
