Pacifico A D, Kirklin J K, Colvin E V, Bargeron L M
Circulation. 1986 Sep;74(3 Pt 2):I53-60.
Uncertainty currently exists as to the optimal definitive procedure for treatment of patients with the Taussig-Bing heart and related cardiac anomalies. Between December 1, 1981 and October 1, 1985, we have used a completely intraventricular tunnel repair, without the use of an extracardiac conduit, in nine patients between 1 and 33 months of age. There was one hospital death from low cardiac output in a 1-month-old infant and one late death 11 months after repair from preexisting and progressive right ventricular cardiomyopathy. Six patients had the Taussig-Bing heart and three had transposition of the great arteries with a ventricular septal defect (VSD). The specific type of tunnel used was determined by the intracardiac anatomy and VSD enlargement was necessary in six patients. Three reoperations were required, two for recurrent VSD between 1 and 3 months after repair and one for tricuspid valve replacement in the patient with right ventricular cardiomyopathy 6 months later. The remaining seven patients are in NYHA class I 1.3 to 47 months postoperatively. We conclude that continued and perhaps expanded use of this technique is appropriate.
目前,对于治疗陶西格-宾氏心脏及相关心脏畸形患者的最佳确定性手术方法尚存在不确定性。在1981年12月1日至1985年10月1日期间,我们对9名年龄在1至33个月的患者采用了完全心室内隧道修复术,未使用心外管道。一名1个月大的婴儿因低心输出量在医院死亡,一名患者在修复术后11个月因原有进行性右心室心肌病晚期死亡。6例患者为陶西格-宾氏心脏,3例为大动脉转位合并室间隔缺损(VSD)。所使用的隧道具体类型由心内解剖结构决定,6例患者需要扩大室间隔缺损。需要进行3次再次手术,2次是因为修复术后1至3个月出现复发性室间隔缺损,1次是6个月后为患有右心室心肌病的患者进行三尖瓣置换。其余7例患者术后1.3至47个月心功能处于纽约心脏协会(NYHA)I级。我们得出结论,继续甚至扩大使用该技术是合适的。