Stringel G
J Pediatr Surg. 1986 Aug;21(8):667-70. doi: 10.1016/s0022-3468(86)80382-7.
Extensive aganglionosis including the ileum occurs in less than 5% of children with Hirschsprung's disease; in these cases nutrition, fluid, and electrolyte balance are a problem. The author reports an infant with extensive aganglionosis including the ileum in whom an endorectal pull-through of the Soave type as modified by Boley was performed with a longitudinal side-to-side anastomosis between the aganglionic and normal intestine, preserving terminal ileum and ileocecal valve. At two and one-half years of age the infant is well. He is toilet trained and has 1 to 4 soft bowel movements per day as he is in the 50th percentile for weight. When extensive aganglionosis involves the small intestine, saving the important function of the terminal ileum and the ileocecal valve is possible and highly desirable.
患有先天性巨结肠症的儿童中，回肠等出现广泛无神经节症的情况不到5%；在这些病例中，营养、液体和电解质平衡是个问题。作者报告了一名患有包括回肠在内的广泛无神经节症的婴儿，对其实施了经直肠结肠拖出术（Boley改良的Soave术式），在无神经节肠段与正常肠段之间进行纵向侧侧吻合，保留了回肠末端和回盲瓣。该婴儿两岁半时情况良好。他已接受如厕训练，体重处于第50百分位，每天有1至4次软便。当广泛无神经节症累及小肠时，保留回肠末端和回盲瓣的重要功能是可行且非常必要的。
