Balagobi B, Abiharan P, Nalini R, Chrishanthi R, Theepan J, Heerthikan K
Department of Surgery, Faculty of Medicine, University of Jaffna, Sri Lanka.
University Surgical Unit, Teaching Hospital Jaffna, Sri Lanka.
Int J Surg Case Rep. 2023 Aug;109:108505. doi: 10.1016/j.ijscr.2023.108505. Epub 2023 Jul 16.
Primary urethral carcinoma is a rare disease with overall poorer outcomes in the past. It is relatively more uncommon in female sex.
We present a case of a female with primary urethral carcinoma that presented atypically as a vulval mass without any features of storage, voiding lower urinary tract symptoms, or gross haematuria.
As primary urethral carcinoma is rare in occurrence, prospective studies are limited so as the recommendations to guide treatment options. Treatment recommendations are still on development from different small-scale studies as well as from data in higher volume centers. Management options depends on location, extent, histology of the lesion as well as on sex of the patient and fitness of the patient.
Early diagnosis and treatment with multidisciplinary consult and multimodality will improve the overall survival rate and quality of life of the patients.
原发性尿道癌是一种罕见疾病，过去总体预后较差。在女性中相对更不常见。
我们报告一例原发性尿道癌女性病例，该病例表现不典型，为外阴肿块，无任何储尿、排尿相关下尿路症状或肉眼血尿特征。
由于原发性尿道癌发病率低，前瞻性研究有限，因此指导治疗选择的建议也有限。不同的小规模研究以及大容量中心的数据仍在不断完善治疗建议。治疗方案取决于病变的位置、范围、组织学类型以及患者的性别和身体状况。
早期诊断并通过多学科会诊和多模式治疗将提高患者的总体生存率和生活质量。
