宫颈血管周上皮样细胞瘤：一种罕见肿瘤诊断与预后的挑战
Cervical PEComa: Challenges in diagnosis and prognosis of a rare neoplasm.
作者信息
Mah Sarah J, Hoang Lien, Lee Shaina, Finlayson Sarah, Carey Mark S
机构信息
Department of Obstetrics and Gynecology, McMaster University, Hamilton, ON, Canada.
Department of Anatomical Pathology, University of British Columbia, Vancouver General Hospital, Vancouver, BC, Canada.
出版信息
Gynecol Oncol Rep. 2023 Jul 7;48:101238. doi: 10.1016/j.gore.2023.101238. eCollection 2023 Aug.
•Cervical PEComas are rare neoplasms which present a diagnostic challenge.•Large tumour size is an important clinical prognosticator in cervical PEComa.•All reported cases of cervical PEComa classified as benign by Folpe criteria behaved in benign fashion clinically.•Tumours ≤ 4 cm may be assessed with cone biopsy, and simple hysterectomy considered if no adverse pathologic features.•Molecular characterization and linkage with coordinated rare tumour registries may identify novel treatments.
•宫颈血管周上皮样细胞瘤（PEComa）是罕见肿瘤，诊断具有挑战性。
•肿瘤体积大是宫颈PEComa重要的临床预后指标。
•所有根据福尔佩标准分类为良性的宫颈PEComa报告病例临床行为均为良性。
•直径≤4cm的肿瘤可行锥形活检评估，若无不良病理特征可考虑单纯子宫切除术。
•分子特征分析以及与罕见肿瘤协作登记系统的关联可能会确定新的治疗方法。
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