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先天性心脏横纹肌瘤:产前超声心动图检测、围产期管理及手术治疗

Congenital intracardiac rhabdomyoma: prenatal detection by echocardiography, perinatal management, and surgical treatment.

作者信息

Boxer R A, Seidman S, Singh S, LaCorte M A, Pek H, Goldman M A, Parnell V

出版信息

Am J Perinatol. 1986 Oct;3(4):303-5. doi: 10.1055/s-2007-999884.

DOI:10.1055/s-2007-999884
PMID:3755913
Abstract

A case of a newborn infant with an intracardiac tumor, detected in utero by fetal echocardiography at 30 weeks gestation, is presented. The prenatal evaluation by serial fetal echocardiograms and nonstress tests is described. In the perinatal period, ventricular tachycardia occurred and was successfully managed with antiarrhythmic medications. At 20 months of age, a right ventricular rhabdomyoma was removed at open heart surgery. The patient represents the earliest in utero detection of a fetal intracardiac tumor with successful postnatal outcome.

摘要

本文报告一例新生儿心脏内肿瘤病例,该病例在妊娠30周时通过胎儿超声心动图在子宫内被检测到。描述了通过系列胎儿超声心动图和无应激试验进行的产前评估。在围产期,发生了室性心动过速,并通过抗心律失常药物成功治疗。在20个月大时,通过心脏直视手术切除了右心室横纹肌瘤。该患者代表了子宫内最早检测到的胎儿心脏内肿瘤且产后预后成功的病例。

相似文献

1
Congenital intracardiac rhabdomyoma: prenatal detection by echocardiography, perinatal management, and surgical treatment.先天性心脏横纹肌瘤:产前超声心动图检测、围产期管理及手术治疗
Am J Perinatol. 1986 Oct;3(4):303-5. doi: 10.1055/s-2007-999884.
2
Cardiac rhabdomyoma: surgical treatment in the neonate.
J Thorac Cardiovasc Surg. 1984 May;87(5):725-31.
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[Resection of a cardiac rhabdomyoma of the right and left ventricular outflow tract].[右心室和左心室流出道心脏横纹肌瘤切除术]
Z Kardiol. 1989 Sep;78(9):607-10.
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A giant rhabdomyoma with left ventricular inflow occlusion and univentricular physiology.一例伴有左心室流入道梗阻及单心室生理状态的巨大横纹肌瘤。
Thorac Cardiovasc Surg. 2005 Aug;53(4):259-60. doi: 10.1055/s-2005-865603.
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Giant Rhabdomyoma Requiring Emergency Resection Early After Birth.出生后早期需紧急切除的巨大横纹肌瘤。
Ann Thorac Surg. 2019 Jan;107(1):e65. doi: 10.1016/j.athoracsur.2018.05.093.
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Difficulty of fetal monitoring in a fetus with intracardiac tumors.
Obstet Gynecol. 1989 Mar;73(3 Pt 2):477-81.
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[Rhabdomyoma of the left atrium. A rare case of mitral valve congenital obstruction simulating hypoplastic left heart syndrome. Echocardiographic diagnosis].
G Ital Cardiol. 1982;12(6):442-4.
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Prenatal diagnosis of intracardiac rhabdomyoma: a case report.心脏横纹肌瘤的产前诊断:一例报告
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[Rhabdomyoma of the heart: three case report (author's transl)].心脏横纹肌瘤:三例报告(作者译)
An Esp Pediatr. 1982 Feb;16(2):163-9.

引用本文的文献

1
Fetal and neonatal cardiac tumors.胎儿及新生儿心脏肿瘤。
Pediatr Cardiol. 2004 May-Jun;25(3):252-73. doi: 10.1007/s00246-003-0590-4.