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1例接受类固醇治疗的神经元核内包涵体病患者出现罕见肾脏表现的病例。

A case of unusual renal manifestation in a patient with neuronal intranuclear inclusion disease treated with steroids.

作者信息

Morita Keisuke, Shinzato Takahiro, Endo Yuzo, Suzuki Makoto, Yoshida Hidefumi, Sone Jun, Nagai Kojiro

机构信息

Department of Nephrology Shizuoka General Hospital Shizuoka Japan.

Department of Diagnostic Pathology Shizuoka General Hospital Shizuoka Japan.

出版信息

Clin Case Rep. 2023 Aug 8;11(8):e7730. doi: 10.1002/ccr3.7730. eCollection 2023 Aug.

DOI:10.1002/ccr3.7730
PMID:37564608
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10410123/
Abstract

Neuronal intranuclear inclusion disease (NIID) is a progressive neurodegenerative disorder characterized by intranuclear inclusions. Kidney injury involvement and successful treatment for NIID have rarely been reported. A NIID patient developed crescentic IgA nephropathy. Steroid therapy resolved digestive symptoms and recovered renal function. Steroids are considered for concomitant symptoms of NIID.

摘要

神经元核内包涵体病（NIID）是一种以核内包涵体为特征的进行性神经退行性疾病。肾脏损伤受累及NIID的成功治疗鲜有报道。一名NIID患者发生了新月体性IgA肾病。类固醇治疗缓解了消化症状并恢复了肾功能。对于NIID的伴随症状可考虑使用类固醇。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/607c/10410123/c4e01feb6238/CCR3-11-e7730-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/607c/10410123/143cf9f289aa/CCR3-11-e7730-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/607c/10410123/7ac742e6e27b/CCR3-11-e7730-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/607c/10410123/c4e01feb6238/CCR3-11-e7730-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/607c/10410123/143cf9f289aa/CCR3-11-e7730-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/607c/10410123/7ac742e6e27b/CCR3-11-e7730-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/607c/10410123/c4e01feb6238/CCR3-11-e7730-g002.jpg

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