Jansz Jacqueline, Tran Huynh W, Sweiss Nadera J
Internal Medicine, University of Illinois at Chicago, Chicago, USA.
Rheumatology, Wynn Medical Center, Rosemead, USA.
Cureus. 2023 Jul 14;15(7):e41879. doi: 10.7759/cureus.41879. eCollection 2023 Jul.
Clinically amyopathic dermatomyositis (CADM) is a rare form of dermatomyositis. Patients with this condition present with the typical skin findings of dermatomyositis but lack the characteristic muscle weakness associated with dermatomyositis. This case presentation highlights the unusual clinical manifestation of CADM in a 49-year-old Vietnamese female. The patient initially presented with persistent hyperpigmented plaques on her hands, which did not respond to the standard treatment for atopic dermatitis. The patient later developed respiratory failure and lung fibrosis in Vietnam. This case underscores the challenges in diagnosing and managing CADM, particularly in patients with atypical presentations, and emphasizes the difficulties in managing such cases of CADM in the community setting.
临床无肌病性皮肌炎(CADM)是皮肌炎的一种罕见形式。患有这种疾病的患者表现出皮肌炎典型的皮肤表现,但缺乏与皮肌炎相关的特征性肌肉无力。本病例报告突出了一名49岁越南女性CADM的不寻常临床表现。患者最初双手出现持续性色素沉着斑,对特应性皮炎的标准治疗无反应。该患者后来在越南出现呼吸衰竭和肺纤维化。本病例强调了CADM诊断和管理中的挑战,特别是在非典型表现的患者中,并强调了在社区环境中管理此类CADM病例的困难。