Brignolio F, Leone M, Tribolo A, Rosso M G, Meineri P, Schiffer D
Ital J Neurol Sci. 1986 Aug;7(4):431-5. doi: 10.1007/BF02283021.
A descriptive epidemiological survey of hereditary ataxias and spastic paraplegias was conducted in the province of Torino, Italy (2,327 996 inhabitants). On prevalence day (31 December 1982) 142 patients were alive. Total prevalence was 6.1 cases/100,000 inhabitants (95% confidence limits = 5.1-7.0). The prevalence rate was 2.6 for recessive or sporadic juvenile ataxias, 1.3 for spastic paraplegias, 1.2 for autosomal dominant cerebellar ataxias, and 1.1 for late onset cerebellar ataxias. The prevalence of hereditary ataxias is similar in our province to that recorded in other populations, but hereditary spastic paraplegias are less frequent than in other populations.
在意大利都灵省（有2327996名居民）开展了一项关于遗传性共济失调和痉挛性截瘫的描述性流行病学调查。在患病率调查日（1982年12月31日），有142名患者存活。总患病率为6.1例/10万居民（95%置信区间=5.1 - 7.0）。隐性或散发性青少年共济失调的患病率为2.6，痉挛性截瘫为1.3，常染色体显性小脑共济失调为1.2，迟发性小脑共济失调为1.1。我们省遗传性共济失调的患病率与其他人群记录的相似，但遗传性痉挛性截瘫比其他人群少见。
