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Emergency cesarean section in glanzmann thrombasthenia: Anaesthetic management without recombinant factor VIIa.血小板无力症患者的急诊剖宫产：未使用重组凝血因子VIIa的麻醉管理
Saudi J Anaesth. 2023 Jul-Sep;17(3):407-409. doi: 10.4103/sja.sja_753_22. Epub 2023 Jun 22.
2
Intensive menstrual bleeding successfully treated with recombinant factor VIIa in Glanzmann thrombasthenia.在 Glanzmann 血小板无力症中，重组因子 VIIa 成功治疗了重度月经过多。
Clin Appl Thromb Hemost. 2011 Aug;17(4):320-2. doi: 10.1177/1076029610364518. Epub 2010 May 11.
3
[Postpartum hemorrhage successfully treated with recombinant factor VIIa in Glanzmann thromboasthenia].[重组凝血因子VIIa成功治疗血小板无力症患者产后出血]
Rinsho Ketsueki. 2008 Jan;49(1):46-50.
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New Insights Into the Treatment of Glanzmann Thrombasthenia.对血小板无力症治疗的新见解
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Low Concentrations of Recombinant Factor VIIa May Improve the Impaired Thrombin Generation of Glanzmann Thrombasthenia Patients.低浓度重组 VII 因子可能改善 Glanzmann 血小板无力症患者受损的凝血酶生成。
Thromb Haemost. 2019 Jan;119(1):117-127. doi: 10.1055/s-0038-1676348. Epub 2018 Dec 31.
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The use of recombinant factor VIla in a primigravida with Glanzmann's thrombasthenia during delivery.重组凝血因子VIIa在一名患有Glanzmann血小板无力症的初产妇分娩期间的应用。
J Perinat Med. 2004;32(5):456-8. doi: 10.1515/JPM.2004.147.
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Pyelolithotomy in a patient with Glanzmann thrombasthenia and antiglycoprotein IIb/IIIa antibodies: the shortest possible duration of treatment with recombinant activated factor VII and platelet transfusions.患有Glanzmann血小板无力症和抗糖蛋白IIb/IIIa抗体患者的肾盂切开取石术：重组活化因子VII和血小板输注的最短治疗时长
Turk J Pediatr. 2003 Jan-Mar;45(1):64-6.
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The use of recombinant FVIIa in a patient with Glanzmann thrombasthenia with uncontrolled bleeding after tonsillectomy.重组凝血因子VIIa在一名患Glanzmann血小板无力症且扁桃体切除术后出血无法控制的患者中的应用。
Blood Coagul Fibrinolysis. 2009 Apr;20(3):215-7. doi: 10.1097/MBC.0b013e32831d0f69.
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Successful management of perioperative hemostasis in a patient with Glanzmann thrombasthenia who underwent a right total mastectomy.对一名患有Glanzmann血小板无力症并接受了右侧全乳切除术的患者进行围手术期止血的成功管理。
Int J Hematol. 2017 Feb;105(2):221-225. doi: 10.1007/s12185-016-2096-x. Epub 2016 Oct 1.
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Weekly low-dose recombinant factor VIIa prophylaxis in Glanzmann thrombasthenia.每周给予低剂量重组 VII 因子预防治疗 Glanzmann 血小板无力症。
Blood Coagul Fibrinolysis. 2021 Jul 1;32(5):349-351. doi: 10.1097/MBC.0000000000001026.

本文引用的文献

1
How I manage pregnancy in women with Glanzmann thrombasthenia.我如何管理患有Glanzmann血小板无力症的女性的妊娠。
Blood. 2022 Apr 28;139(17):2632-2641. doi: 10.1182/blood.2021011595.
2
Glanzmann thrombasthenia in pregnancy: Optimising maternal and fetal outcomes.妊娠期血小板无力症：优化母婴结局
Obstet Med. 2016 Dec;9(4):169-170. doi: 10.1177/1753495X16655021. Epub 2016 Aug 3.
3
Anaesthetic Management with Thromboelastography in a Patient with Glanzmann Thrombasthenia.一名患有Glanzmann血小板无力症患者的血栓弹力图麻醉管理
Turk J Anaesthesiol Reanim. 2014 Aug;42(4):227-9. doi: 10.5152/TJAR.2014.69077. Epub 2014 May 29.
4
Glanzmann's thrombasthenia: pathogenesis, diagnosis, and current and emerging treatment options.血小板无力症：发病机制、诊断以及当前和新兴的治疗选择。
J Blood Med. 2015 Jul 8;6:219-27. doi: 10.2147/JBM.S71319. eCollection 2015.
5
Rational Use of Recombinant Factor VIIa in Clinical Practice.重组凝血因子VIIa在临床实践中的合理应用
Indian J Hematol Blood Transfus. 2014 Jun;30(2):85-90. doi: 10.1007/s12288-013-0240-9. Epub 2013 Feb 23.
6
Current concepts in platelet transfusion.血小板输注的当前概念。
Asian J Transfus Sci. 2009 Jan;3(1):18-21. doi: 10.4103/0973-6247.45257.

血小板无力症患者的急诊剖宫产：未使用重组凝血因子VIIa的麻醉管理

Emergency cesarean section in glanzmann thrombasthenia: Anaesthetic management without recombinant factor VIIa.

作者信息

Priyanka Andal, Arulprakasam Santhosh, Rudingwa Priya

机构信息

Department of Anaesthesiology and Critical Care, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India.

出版信息

Saudi J Anaesth. 2023 Jul-Sep;17(3):407-409. doi: 10.4103/sja.sja_753_22. Epub 2023 Jun 22.

DOI:10.4103/sja.sja_753_22
PMID:37601512
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10435786/
Abstract

Glanzmann thrombasthenia (GT) is a congenital disorder inherited autosomal recessively, caused by deficiency of platelet membrane glycoprotein IIb-IIIa complex leading to defective platelet aggregation, and manifesting as mucocutaneous bleeding. Parturients with GT requiring emergency cesarean section are at high risk for perioperative bleeding complications. The anesthetist should be prepared with the necessary measures to control bleeding. This paper presents the successful management of a 23-year-old primigravida with GT undergoing cesarean section in a resource-limited setup where thromboelastography and recombinant factor VIIa (rFVIIa) are not available.

摘要

Glanzmann血小板无力症（GT）是一种常染色体隐性遗传的先天性疾病，由血小板膜糖蛋白IIb-IIIa复合物缺乏引起，导致血小板聚集缺陷，并表现为皮肤黏膜出血。患有GT且需要紧急剖宫产的产妇围手术期出血并发症风险很高。麻醉医生应准备好控制出血的必要措施。本文介绍了一名23岁初产妇GT患者在资源有限的情况下进行剖宫产的成功管理，该情况下无法进行血栓弹力图检查和使用重组凝血因子VIIa（rFVIIa）。