Suppr超能文献

伪装成转移瘤的原发性肝脏上皮样血管内皮瘤:1例罕见病例报告

Primary hepatic epithelioid hemangioendothelioma masquerading as metastases: A rare case report.

作者信息

Marak James R, Raj Gaurav, Verma Shashwat, Gandhi Ajeet

机构信息

Department of Radiodiagnosis, Dr RMLIMS, Lucknow, Uttar Pradesh, 226010, India.

Department of Nuclear Medicine, Dr RMLIMS, Lucknow, Uttar Pradesh, 226010, India.

出版信息

Radiol Case Rep. 2023 Aug 11;18(10):3739-3747. doi: 10.1016/j.radcr.2023.07.046. eCollection 2023 Oct.

Abstract

Epithelioid hemangioendothelioma (EHE) of the liver is an extremely rare malignant tumor of vascular origin, representing less than 1 % of all vascular tumors. Nearly 260 cases have been reported in English literature. Radiologically it is seen as multifocal lesions. It can be seen at different sites like lungs, bones, lymph nodes, breasts, and soft tissue. Often it is misdiagnosed with metastases, cholangiocarcinoma, or angiosarcoma. No definite treatment protocol is available due to its rarity, however, these malignancies are treated by radical resection of the tumor or liver transplant and/or chemotherapy. Here we present a primary hepatic epithelioid hemangioendothelioma (HEHE) which was mimicking metastases in a 42-year-old male who was treated with chemotherapy and radiotherapy. Sadly the patient expired after 1 year of complete course of treatment. Imaging features can help to improve the diagnostic accuracy of this tumor.

摘要

肝脏上皮样血管内皮瘤(EHE)是一种极为罕见的血管源性恶性肿瘤,占所有血管肿瘤的比例不到1%。英文文献中已报道了近260例病例。在放射学上,它表现为多灶性病变。它可见于不同部位,如肺、骨、淋巴结、乳房和软组织。它常被误诊为转移瘤、胆管癌或血管肉瘤。由于其罕见性,尚无明确的治疗方案,然而,这些恶性肿瘤通过肿瘤根治性切除或肝移植和/或化疗进行治疗。在此,我们报告一例原发性肝脏上皮样血管内皮瘤(HEHE),该病例在一名42岁男性中表现为类似转移瘤,患者接受了化疗和放疗。遗憾的是,患者在完成整个疗程1年后死亡。影像学特征有助于提高该肿瘤的诊断准确性。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3da2/10440529/6b574a6c3b71/gr1.jpg

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验