Jain Ankit, Lone Yasir Ahmad
Department of General Surgery, Himalayan Institute of Medical Sciences, Swami Rama Himalayan University, Dehradun, Uttarakhand, India.
Department of Pediatric Surgery, Himalayan Institute of Medical Sciences, Swami Rama Himalayan University, Dehradun, Uttarakhand, India.
J Indian Assoc Pediatr Surg. 2023 Jul-Aug;28(4):348-351. doi: 10.4103/jiaps.jiaps_8_23. Epub 2023 Jul 11.
Urethral duplication is a rare anomaly with varying clinical manifestations. About 300 cases have been reported till date and are often associated with genitourinary (GU) and gastrointestinal (GI) tract anomalies. A 6-day-old neonate presented with an absent anal opening and a tiny perineal fistula having slight meconium staining. He did well after anoplasty. Low anorectal malformation (ARM) has been reported as the GI anomaly associated with urethral duplication. However, an ectopic scrotum as the principal GU tract anomaly associated with urethral duplication is being reported for the first time in literature with probable embryologic explanation. The GU tract anomalies were successfully repaired surgically later in infancy.
尿道重复是一种罕见的异常情况,临床表现各异。迄今为止已报道约300例,常与泌尿生殖系统(GU)和胃肠道(GI)异常相关。一名6天大的新生儿出现肛门开口缺失和一个有轻微胎粪染色的小会阴瘘。肛门成形术后情况良好。低位肛门直肠畸形(ARM)已被报道为与尿道重复相关的胃肠道异常。然而,异位阴囊作为与尿道重复相关的主要泌尿生殖系统异常在文献中首次被报道,并给出了可能的胚胎学解释。泌尿生殖系统异常在婴儿期后期通过手术成功修复。