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小儿左心耳动脉瘤:病例研究与文献综述

Left atrial appendage aneurysm in pediatrics: Case study and literature review.

作者信息

Norozi Kambiz, Subasri Mathushan, Diaz Luis Altamirano, Honjo Osami

机构信息

Department of Paediatrics, University of Western Ontario, London, ON, Canada.

Division of Pediatric Cardiology, Department of Paediatrics, London Health Sciences Centre, London, ON, Canada.

出版信息

Front Cardiovasc Med. 2023 Aug 10;10:1211619. doi: 10.3389/fcvm.2023.1211619. eCollection 2023.

DOI:10.3389/fcvm.2023.1211619
PMID:37636313
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10449248/
Abstract

Left atrial appendage aneurysm (LAAA) is a rare cardiac pathology that is often identified in adulthood. There are a myriad of presentations related to atrial appendage enlargement, but most are asymptomatic. Pediatric cases of LAAA are extremely rare. We report a case of an incidental giant LAAA found in a healthy 6-year-old boy. He was successfully treated with surgical resection. A review of the literature shows that the presentation of LAAA in pediatrics likely involves cardiac or respiratory symptoms but can also be incidental findings. Similar to adults, diagnosis requires cardiac imaging, with echocardiography being the mainstay. Surgical intervention is indicated in symptomatic and most asymptomatic patients to prevent complications. More research is warranted into the optimal timing of surgery and alternative surgical approaches for complex cases.

摘要

左心耳动脉瘤(LAAA)是一种罕见的心脏疾病,常在成年期被发现。与心耳扩大相关的表现多种多样,但大多数无症状。小儿LAAA病例极为罕见。我们报告一例在一名健康6岁男孩中偶然发现的巨大LAAA病例。他通过手术切除成功治愈。文献回顾显示,小儿LAAA的表现可能涉及心脏或呼吸系统症状,但也可能是偶然发现。与成人相似,诊断需要心脏成像,超声心动图是主要手段。有症状和大多数无症状患者均需手术干预以预防并发症。对于复杂病例的最佳手术时机和替代手术方法,仍需更多研究。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dbf9/10449248/892e5c55bac7/fcvm-10-1211619-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dbf9/10449248/892e5c55bac7/fcvm-10-1211619-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dbf9/10449248/892e5c55bac7/fcvm-10-1211619-g001.jpg

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2
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3
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Echocardiography. 2021 Oct;38(10):1809-1812. doi: 10.1111/echo.15192. Epub 2021 Sep 12.
4
Thoracoscopic Resection of Left Atrial Appendage Aneurysm in a 16-Year-Old Boy.16 岁男孩行胸腔镜左心耳动脉瘤切除术
Ann Thorac Surg. 2021 Dec;112(6):e451-e453. doi: 10.1016/j.athoracsur.2021.02.049. Epub 2021 Mar 4.
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