Belcourt C L, Roy D L, Nanton M A, Finley J P, Gillis D A, Krause V W, Aterman K
Radiology. 1986 Oct;161(1):109-12. doi: 10.1148/radiology.161.1.3763852.
Congenital stenosis of individual pulmonary veins is uncommon. Of the 49 cases reported, four were seen at the IWK Hospital for Children and are reported here. Plain radiographs show a shift of the heart toward the side of major involvement, Kerley B lines, fluid in the fissures, and interstitial edema of the affected lobes. These findings, while subtle, should nevertheless suggest stenosis. Technetium-99m macro-aggregate lung perfusion scans show absence of or diminished perfusion of the affected lobes. The diagnosis can usually be confirmed with angiography. Congenital stenosis of individual pulmonary veins should be considered in children with repeated pulmonary infections, dyspnea, failure to thrive, hemoptysis, or unexplained pulmonary hypertension.
先天性单支肺静脉狭窄并不常见。在已报道的49例病例中，有4例在伊维克儿童医院被发现，现于此报道。胸部X线平片显示心脏向主要受累侧移位、克氏B线、叶间裂积液以及受累肺叶的间质水肿。这些表现虽然细微，但仍应提示存在狭窄。锝-99m大聚合体肺灌注扫描显示受累肺叶灌注缺失或减少。通常通过血管造影可确诊。对于反复发生肺部感染、呼吸困难、生长发育不良、咯血或不明原因肺动脉高压的儿童，应考虑先天性单支肺静脉狭窄。
