Bunul Sena Destan
Neurology, Kocaeli University, Kocaeli, TUR.
Cureus. 2023 Sep 1;15(9):e44504. doi: 10.7759/cureus.44504. eCollection 2023 Sep.
Objective To compare the initial presentation, clinical features, disease courses, and radiological parameters between familial multiple sclerosis (fMS) and sporadic multiple sclerosis (sMS) to determine if the two represent distinct clinical entities. Methods This retrospective study was conducted at the Neurology Clinic at Kocaeli University Hospital. Records of 114 fMS and 150 sMS patients, aged 18-65, diagnosed based on either the Poser criteria or the McDonald 2001 criteria were analyzed. Radiological data and Expanded Disability Status Scale (EDSS) evaluations were conducted by a specialist neurologist. Variables included age at MS onset, first symptoms, relapses, EDSS scores at diagnosis and last examination, and MRI findings. Statistical Package for the Social Sciences (IBM SPSS Statistics for Windows, IBM Corp., Version 28, Armonk, NY) was utilized for data analysis. Results Both fMS and sMS groups were comparable in age (43.55±12.50 and 42.35±10.61 years, respectively) and gender distribution (females: fMS 71.9%, sMS 71.3%). No significant difference was noted regarding disease onset age (fMS 29.83±10.77, sMS 30.42±9.7). Age of onset, final EDSS, and relapse rate didn't significantly vary among sMS, fMS with first-degree relatives having MS (fMS(1)), and fMS with second or third-degree relatives having MS (fMS(2)). The fMS group showed a significantly higher incidence of initial spinal cord lesions on MRI compared to the sMS group (38.6% vs. 17.3%; p<0.001). Within the fMS group, the presence of spinal cord lesions on initial MRI correlated with a higher relapse rate and elevated initial and final EDSS scores. Conclusion Despite overarching similarities between fMS and sMS, spinal cord lesions' prevalence and implications in fMS may point to a genetic underpinning warranting in-depth exploration.
目的 比较家族性多发性硬化(fMS)和散发性多发性硬化(sMS)之间的首发表现、临床特征、病程及影像学参数,以确定两者是否代表不同的临床实体。方法 本回顾性研究在科贾埃利大学医院神经科门诊进行。分析了114例fMS患者和150例sMS患者的记录,这些患者年龄在18至65岁之间,根据波塞标准或2001年麦克唐纳标准确诊。由一名神经科专科医生进行影像学数据和扩展残疾状态量表(EDSS)评估。变量包括MS发病年龄、首发症状、复发情况、诊断时和末次检查时的EDSS评分以及MRI表现。使用社会科学统计软件包(IBM SPSS Statistics for Windows,IBM公司,第28版,纽约州阿蒙克)进行数据分析。结果 fMS组和sMS组在年龄(分别为43.55±12.50岁和42.35±10.61岁)和性别分布(女性:fMS组71.9%,sMS组71.3%)方面具有可比性。在疾病发病年龄方面未观察到显著差异(fMS组29.83±10.77,sMS组30.42±9.7)。在sMS、有一级亲属患MS的fMS(fMS(1))和有二级或三级亲属患MS的fMS(fMS(2))之间,发病年龄、最终EDSS评分和复发率没有显著差异。与sMS组相比,fMS组MRI上初始脊髓病变的发生率显著更高(38.6%对17.3%;p<0.001)。在fMS组中,初始MRI上脊髓病变的存在与更高的复发率以及初始和最终EDSS评分升高相关。结论 尽管fMS和sMS之间存在总体相似性,但fMS中脊髓病变的患病率及其影响可能表明存在遗传基础,值得深入探索。