Med Sidi El Moctar Echreiva, El Hadj Sidi Chighaly, Abdulrazzak Mohammed, Ahmed Kamal Manar, Mohamed Ahmed Mohamed Feissal, Boye Khaled
Faculty of Medicine, Ain Shams University, Cairo.
Center National de Cardiology, Nouakchott, Mauritania.
Ann Med Surg (Lond). 2023 Jul 31;85(9):4593-4596. doi: 10.1097/MS9.0000000000001116. eCollection 2023 Sep.
Right atrial myxoma is rarely associated with Budd-Chiari syndrome (BCS). In this paper, we present a case of a young patient with a giant right atrial myxoma complicated by the development of BCS.
A 26-year-old female presented to the emergency room with persistent abdominal pain, ascites, lower limb edema, and an acute episode of dyspnea. Abdominal computed tomography revealed a lesion in the right cardiac cavity that resembled an intracardiac thrombus. Transthoracic echocardiography showed a large heterogeneous mass in the right atrium protruding into the right ventricle and a large thrombus interfering with inferior vena cava flow. The patient underwent cardiac surgery to remove the atrial mass, and histopathologic examinations confirmed the diagnosis of atrial myxoma.
The right atrial myxoma is relatively rare, especially the giant ones. Rarely have intracardiac tumors such as giant right atrial myxoma been identified as a risk factor for the onset of BCS.
In the differential diagnosis of BCS, right atrial tumors, including myxomas, should be considered, especially when other explanations are absent.
右心房黏液瘤很少与布加综合征(BCS)相关。在本文中,我们报告一例年轻患者,患有巨大右心房黏液瘤并并发布加综合征。
一名26岁女性因持续性腹痛、腹水、下肢水肿及急性呼吸困难发作就诊于急诊室。腹部计算机断层扫描显示右心腔内有一病变,类似心内血栓。经胸超声心动图显示右心房内有一巨大不均匀肿块突入右心室,并有一巨大血栓干扰下腔静脉血流。患者接受了心脏手术以切除心房肿块,组织病理学检查确诊为心房黏液瘤。
右心房黏液瘤相对少见,尤其是巨大型。像巨大右心房黏液瘤这样的心内肿瘤很少被确定为布加综合征发病的危险因素。
在布加综合征的鉴别诊断中,应考虑包括黏液瘤在内的右心房肿瘤,尤其是在没有其他解释的情况下。