Bagheri Abbas, Feizi Mohadeseh, Tavakoli Mehdi
Ocular Tissue Engineering Research Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
Ophthalmic Research Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
J Curr Ophthalmol. 2023 Aug 11;35(1):93-95. doi: 10.4103/joco.joco_153_22. eCollection 2023 Jan-Mar.
To report surgical repair of a rare case of Tessier number 9 craniofacial cleft.
Case report.
Tessier number 9 craniofacial cleft is the rarest cleft anomaly. This article reports a congenital eyelid coloboma in a 21-year-old woman that involved the lateral third of the left upper eyelid and extended to the lateral canthus, consistent with number 9 craniofacial cleft Tessier classification. The additional findings included a fibrotic band between the globe and the remnant of the upper lid, which caused a small-angle exotropia. There were also skin appendages in the preauricular area and the inner surface of the nasal columella consistent with Goldenhar syndrome. The eyelid coloboma was repaired by releasing the adhesions and using a composite graft of the hard palate to repair the posterior lamella. The anterior lamella was repaired by creating a skin advancement flap. The esthetic and functional outcomes were acceptable in the 2-year postoperative follow-up period.
The composite hard palate graft can be used to repair posterior lamella defect in the case of Tessier number 9 craniofacial cleft.
报告1例罕见的第9号Tessier颅面裂的手术修复情况。
病例报告。
第9号Tessier颅面裂是最罕见的颅面裂畸形。本文报道1例21岁女性的先天性眼睑缺损，累及左上眼睑外侧三分之一并延伸至外眦，符合第9号颅面裂的Tessier分类。其他发现包括眼球与上睑残余部分之间的纤维化带，导致小角度外斜视。耳前区和鼻小柱内表面也有皮肤附属器，符合Goldenhar综合征。通过松解粘连并使用硬腭复合移植物修复后层来修复眼睑缺损。通过制作皮肤推进皮瓣修复前层。术后2年随访期的美学和功能效果可接受。
对于第9号Tessier颅面裂病例，硬腭复合移植物可用于修复后层缺损。
