Ghantous Imad, Najjar Aziz, Tlaiss Yehya, Danaf Samer, Chouairy Camil J
Urology, Saint George University Hospital in Beirut, Beirut, LBN.
Urology, University of Balamand, Beirut, LBN.
Cureus. 2023 Aug 9;15(8):e43185. doi: 10.7759/cureus.43185. eCollection 2023 Aug.
Extra-adrenal pheochromocytomas are rare catecholamine-producing tumors that arise from chromaffin cells outside the adrenal glands. We report on the case of a 62-year-old male who initially presented with upper respiratory tract symptoms and was found to have a suprapubic pelvic mass and an asymptomatic right inguinal hernia. The diagnostic evaluation involved an abdominal ultrasound, a CT scan, followed by an MRI, which revealed a well-marginated large mass whose characteristics indicated a retroperitoneal sarcoma. Upon successful surgical resection, the mass was found to be encapsulated and no peripheral structure invasion was present; the right inguinal hernia was repaired, and a double J-stent was placed. Histopathological examination revealed extra-adrenal pheochromocytoma. This case report sheds light on diagnostic and therapeutic challenges when dealing with extra-adrenal pheochromocytomas and the importance of considering them as a differential diagnosis when presented with a case of retroperitoneal mass.
肾上腺外嗜铬细胞瘤是一种罕见的分泌儿茶酚胺的肿瘤，起源于肾上腺外的嗜铬细胞。我们报告了一例62岁男性病例，该患者最初表现为上呼吸道症状，随后发现耻骨上盆腔肿块和无症状的右侧腹股沟疝。诊断评估包括腹部超声、CT扫描，随后进行MRI检查，结果显示一个边界清晰的大肿块，其特征提示为腹膜后肉瘤。成功手术切除后，发现肿块有包膜，未侵犯周围结构；右侧腹股沟疝得到修复，并放置了双J支架。组织病理学检查显示为肾上腺外嗜铬细胞瘤。本病例报告揭示了处理肾上腺外嗜铬细胞瘤时的诊断和治疗挑战，以及在遇到腹膜后肿块病例时将其作为鉴别诊断的重要性。
