Sanchez-Quiros Julia, Giralt Lena, Fonollosa Alejandro, Robles Ignacio, Carreño Ester
Department of Ophthalmology, Rey Juan Carlos University Hospital, Madrid, Spain.
Department of Ophthalmology, Hospital Clinic of Barcelona (ICOF), Barcelona, Spain.
Clin Ophthalmol. 2023 Sep 4;17:2625-2630. doi: 10.2147/OPTH.S404644. eCollection 2023.
Tubulointerstitial nephritis and uveitis (TINU) syndrome is a rare autoimmune disease with unclear pathogenesis but probably related to a combination of genetic predisposition and environmental triggers. Diagnosis is challenging due to the asynchronous onset of renal and ocular symptoms, and it is necessary to exclude other causes of nephritis and uveitis. It affects both sexes, with an overall predominance of females and a median age of onset of 15 years. TINU syndrome is characterized by bilateral, non-granulomatous anterior uveitis and tubulointerstitial nephritis, which can cause acute renal failure in severe cases. Several triggers have been identified including concurrent infections, medications, or endocrine diseases. The diagnosis of TINU is mainly based on clinical and analytical findings, and although urinary β2-microglobulin is a useful parameter no specific diagnostic test is available. Current perspectives intend to facilitate its diagnosis identifying susceptibility HLA genotypes, serologic markers and imaging tools to avoid renal biopsy. Treatment options for TINU syndrome include corticosteroids, immunosuppressive agents, and intravenous immunoglobulins, but relapses are frequent, and management can be challenging. The purpose of this review is to provide an updated summary of the diagnostic and treatment strategies of TINU syndrome, helping clinicians recognize and manage this rare autoimmune disorder.
肾小管间质性肾炎伴葡萄膜炎(TINU)综合征是一种罕见的自身免疫性疾病,其发病机制尚不清楚,但可能与遗传易感性和环境触发因素的综合作用有关。由于肾脏和眼部症状的不同步发作,诊断具有挑战性,有必要排除其他引起肾炎和葡萄膜炎的原因。该病男女均可发病,总体上女性更为多见,发病年龄中位数为15岁。TINU综合征的特征是双侧非肉芽肿性前葡萄膜炎和肾小管间质性肾炎,严重时可导致急性肾衰竭。已确定了几种触发因素,包括并发感染、药物或内分泌疾病。TINU的诊断主要基于临床和分析结果,虽然尿β2微球蛋白是一个有用的参数,但尚无特异性诊断测试。当前的观点旨在通过识别易感性HLA基因型、血清学标志物和成像工具来促进其诊断,以避免肾活检。TINU综合征的治疗选择包括皮质类固醇、免疫抑制剂和静脉注射免疫球蛋白,但复发频繁,管理可能具有挑战性。本综述的目的是提供TINU综合征诊断和治疗策略的最新总结,帮助临床医生识别和管理这种罕见的自身免疫性疾病。