Küçük Adem, Mohamed Shukri Said, Abdi Abdishakur Mohamed, Ali Abdullahi Yusuf
Düzce University Faculty of Medicine, Pediatric Surgery Clinic, Düzce 81110, Merkez, Turkey.
Department of Pediatric Surgery, Somali Mogadishu Training and Research Hospital, Mogadishu 0000000, Somalia.
World J Clin Cases. 2023 Sep 16;11(26):6246-6251. doi: 10.12998/wjcc.v11.i26.6246.
Congenital hepatic cysts are relatively rare but are now diagnosed earlier and more frequently with a routine prenatal ultrasound. Solitary liver cysts are divided into simple and solitary intrahepatic biliary cysts, depending on the biliary connection. While some solitary liver cysts are symptomatic in childhood, even in newborns, they are often found incidentally in adults.
A 3-mo-old female infant was admitted to Mogadishu Somali Training and Research Hospital with recurrent vomiting, respiratory problems, and abdominal bloating complaints. On examination, the abdomen was greatly distended and extremely tight. She had repeated vomiting for 3 d, no stool output, and decreased urine. The abdominal ultrasonography detected a solitary cystic lesion measuring 10 cm × 10 cm × 14 cm, extending from the liver or right kidney to the pelvis. In the magnetic resonance imaging examination of the patient, a solitary cystic structure of 10 cm × 10 cm × 14 cm in the right abdomen was observed, extending to the pelvis and possibly originating from the liver. The patient was operated fenestration after her fluid and electrolytes improved. Oral nutrition was initiated on the 2 postoperative day, and the drain was removed on the 5 postoperative day. The patient visited the outpatient clinic control 1 mo later with no clinical complaints.
Congenital liver cysts are usually followed without complications. They rarely reach gigantic dimensions and may cause respiratory distress, intestinal obstruction and recurrent vomiting. Surgery can provide quite successful outcomes in the treatment of giant sized simple liver cysts.
先天性肝囊肿相对少见，但现在通过常规产前超声检查能更早且更频繁地诊断出来。孤立性肝囊肿根据胆管连接情况分为单纯性和孤立性肝内胆管囊肿。虽然一些孤立性肝囊肿在儿童期甚至新生儿期就有症状，但它们常在成人中偶然被发现。
一名3个月大的女婴因反复呕吐、呼吸问题和腹胀主诉入住摩加迪沙索马里培训与研究医院。检查时，腹部极度膨隆且紧绷。她已反复呕吐3天，无排便，尿量减少。腹部超声检查发现一个大小为10 cm×10 cm×14 cm的孤立性囊性病变，从肝脏或右肾延伸至盆腔。在该患者的磁共振成像检查中，观察到右腹部有一个大小为10 cm×10 cm×14 cm的孤立性囊性结构，延伸至盆腔，可能起源于肝脏。患者在液体和电解质状况改善后接受了开窗手术。术后第2天开始经口营养，术后第5天拔除引流管。1个月后患者到门诊复查，无临床不适主诉。
先天性肝囊肿通常无需特殊处理即可随访观察。它们很少发展到巨大尺寸，可能会引起呼吸窘迫、肠梗阻和反复呕吐。手术治疗巨大型单纯肝囊肿可取得相当成功的效果。
