Yoo Seung Jin, Kim Dae Hwan, Cho Seong Hyun, Lee Kyung Ryeol, Seo Kyu Bum
Division of Hand and Microsurgery, Department of Orthopedic Surgery, Jeju National University Hospital, Jeju 63241, Republic of Korea.
Department of Radiology, Jeju National University Hospital, Jeju 63241, Republic of Korea.
Children (Basel). 2023 Sep 21;10(9):1581. doi: 10.3390/children10091581.
Lipofibromatous hamartoma, first reported in 1953, is a rare, slowly progressive soft tissue tumor, the characteristics of which include the enlargement of the affected nerve via the epineurial and perineurial proliferation of adipose and fibrous tissues. Out of 200 previously reported cases of lipofibromatous hamartoma of the median nerve, there have been approximately 25 pediatric cases under the age of 18. Herein, we report a case of lipofibromatous hamatoma of the median nerve in a 3-year-old female patient who was surgically decompressed via carpal tunnel release and epineurolysis. The patient was followed-up on an outpatient clinic basis annually with sonographic evaluations, and the postoperative 10th-year follow-up did not show recurrence or any deficits in motor and sensory functions.
脂肪纤维瘤性错构瘤于1953年首次报道,是一种罕见的、进展缓慢的软组织肿瘤,其特征包括通过神经外膜和神经束膜的脂肪和纤维组织增生导致受累神经增粗。在之前报道的200例正中神经脂肪纤维瘤性错构瘤病例中,约有25例为18岁以下的儿童病例。在此,我们报告一例3岁女性患者的正中神经脂肪纤维瘤性错构瘤,该患者通过腕管松解和神经外膜松解术进行了手术减压。患者每年在门诊接受超声评估随访,术后第10年的随访未显示复发或运动和感觉功能有任何缺陷。