Shekhani Haris N, Hanna Tarek, Johnson Jamlik-Omari
Division of Emergency Radiology, Emory University, Atlanta, GA, USA.
J Radiol Case Rep. 2016 Nov 30;10(11):1-7. doi: 10.3941/jrcr.v10i11.2787. eCollection 2016 Nov.
Lipofibromatous hamartoma is a rare and slow growing benign fibro-fatty tumor. It is characterized by the proliferation of mature adipocytes within the epineurium and the perineurium of the peripheral nerves. In the upper extremity, it most commonly affects the median nerve. Median nerve involvement commonly leads to pain, numbness, paresthesia and carpal tunnel syndrome. This article presents a case of lipofibromatous hamartoma in an 8-year-old child followed by a discussion of the epidemiology, diagnosis, imaging details and treatment options for this condition.
脂肪纤维瘤性错构瘤是一种罕见的、生长缓慢的良性纤维脂肪性肿瘤。其特征是成熟脂肪细胞在周围神经的神经外膜和神经束膜内增生。在上肢,它最常累及正中神经。正中神经受累通常会导致疼痛、麻木、感觉异常和腕管综合征。本文介绍了一例8岁儿童脂肪纤维瘤性错构瘤病例,随后讨论了该疾病的流行病学、诊断、影像学细节和治疗选择。