van de Heyning P H
Acta Otorhinolaryngol Belg. 1978;32(6):671-84.
Cochleo-vestibular dysfunction of patients suffering from a heredo-ataxia, have been frequently described. A family and a single case are presented, which show the association of a heredo-ataxia, more specifically the Roussy-Lévy syndrome, progressive sensorineural loss, nystagmus and vestibular a- or hyporeflexia. A review of the literature is included and the standpoints concerning the nosological entities are discussed.
患有遗传性共济失调的患者的耳蜗 - 前庭功能障碍已被频繁描述。本文介绍了一个家系和一例个案，它们显示了遗传性共济失调，更具体地说是鲁西 - 列维综合征、进行性感音神经性听力损失、眼球震颤和前庭反射减弱或消失之间的关联。文中还包括了文献综述，并讨论了关于疾病分类实体的观点。
