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结节病中的囊性支气管扩张

Cystic bronchiectasis in sarcoidosis.

作者信息

Jadav Raja Shekar, Dadana Sriharsha, Avula Akshay

机构信息

Internal Medicine Cheyenne Regional Medical Center Cheyenne Wyoming USA.

Pulmonology University of Pittsburgh Medical Center Philadeplhia Pennsylvania USA.

出版信息

Clin Case Rep. 2023 Oct 10;11(10):e8045. doi: 10.1002/ccr3.8045. eCollection 2023 Oct.

Abstract

Pulmonary sarcoidosis can manifest in different radiologic patterns. Typical manifestations in high-resolution computed tomography are bilateral perihilar lymphadenopathy, micronodules, and fibrotic changes. Atypical manifestations are mass-like or alveolar opacities, honeycomb-like cysts, miliary opacities, tracheobronchial involvement, and pleural disease. Cystic bronchiectasis in pulmonary sarcoidosis is rare, with only a few reported cases in the literature. We present another case of cystic bronchiectasis with a honeycomb-like pattern in pulmonary sarcoidosis and with cardiac involvement. This case was presented as an abstract poster at the American Thoracic Society conference in 2022.

摘要

肺结节病可表现为不同的放射学模式。高分辨率计算机断层扫描的典型表现为双侧肺门淋巴结肿大、微小结节和纤维化改变。非典型表现为肿块样或肺泡实变、蜂窝状囊肿、粟粒样实变、气管支气管受累及胸膜疾病。肺结节病中的囊性支气管扩张罕见,文献中仅有少数病例报道。我们报告另一例肺结节病合并蜂窝状模式且累及心脏的囊性支气管扩张病例。该病例于2022年在美国胸科学会会议上作为摘要海报展示。

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