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一名青少年患者的阴茎异常勃起与慢性髓性白血病。罕见的首发表现。病例报告。

Priapism and chronic myeloid leukemia in an adolescent. Rare debut presentation. A case report.

作者信息

Romero-Guerra Ana L, Salas-Cosio Miguel de J, Bautista-Martínez Benito A, Castillo-Rodríguez Sebastián A, Landa Juárez Sergio, Hernández-Piñon Zayra, Saldaña Sánchez Iris Del R, Núñez-Enríquez Juan C

机构信息

Department of Schoolchildren and Adolescents; Hospital de Pediatría Centro Médico Nacional Siglo XXI, Instituto Mexicano Del Seguro Social, Federal District, Mexico.

Department of Pediatric Hematology; Hospital de Pediatría Centro Médico Nacional Siglo XXI, Instituto Mexicano Del Seguro Social, Federal District, Mexico.

出版信息

Arch Argent Pediatr. 2024 Apr 1;122(2):e202310068. doi: 10.5546/aap.2023-10068.eng. Epub 2023 Oct 26.

DOI:10.5546/aap.2023-10068.eng
PMID:37871128
Abstract

Priapism is a painful and persistent erection, with or without sexual stimulation. A rare cause of such abnormality is chronic myeloid leukemia. Few cases of priapism as an initial manifestation of this type of leukemia have been reported in adolescent patients. Here we describe the case of a 16-year-old patient who presented with priapism as the initial manifestation of chronic myeloid leukemia. No cavernosal aspiration was performed. A specific hematological treatment was started and, given the persistence of priapism, the patient required 2 corpora cavernosa shunt procedures; despite this treatment, there is a high probability of sequelae.

摘要

阴茎异常勃起是一种伴有或不伴有性刺激的持续性疼痛勃起。慢性髓性白血病是导致这种异常情况的罕见原因。青少年患者中,很少有阴茎异常勃起作为此类白血病初始表现的病例报道。在此,我们描述一名16岁患者,其阴茎异常勃起为慢性髓性白血病的初始表现。未进行海绵体抽吸。开始了特定的血液学治疗,鉴于阴茎异常勃起持续存在,患者需要进行2次海绵体分流手术;尽管进行了这种治疗,但仍有很高的后遗症可能性。

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引用本文的文献

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Ecancermedicalscience. 2025 Feb 27;19:1860. doi: 10.3332/ecancer.2025.1860. eCollection 2025.