Ahuja S, Loffler W, Wegener O H, Ernst H
Urology. 1986 Nov;28(5):413-9. doi: 10.1016/0090-4295(86)90076-2.
This is a case report of a patient with angiomyolipomas in both kidneys which was confirmed in one kidney by open biopsy and histologic examination. Two years after diagnosis of the angiomyolipomatosis, the patient died of metastatic hypernephromas of both kidneys. The tumors had affected the kidneys almost totally; only in the right kidney were remnants of the angiomyolipoma still recognizable. A review of the literature shows how rare is the simultaneous occurrence of angiomyolipomas and hypernephroma.
这是一例双肾血管平滑肌脂肪瘤患者的病例报告，其中一个肾脏经开放性活检和组织学检查得以确诊。血管平滑肌脂肪瘤病诊断两年后，患者死于双肾转移性肾细胞癌。肿瘤几乎完全累及双肾；仅右肾仍可辨认出血管平滑肌脂肪瘤的残余部分。文献回顾显示，血管平滑肌脂肪瘤与肾细胞癌同时发生的情况极为罕见。
