Wedekind Henri, Beimdiek Julia, Rossdam Charlotte, Kats Elina, Wittek Vanessa, Schumann Lisa, Sörensen-Zender Inga, Fenske Arno, Weinhold Birgit, Schmitt Roland, Tiede Andreas, Büttner Falk F R, Münster-Kühnel Anja, Abeln Markus
Institute of Clinical Biochemistry, Hannover Medical School, Hannover, Germany.
Department of Nephrology and Hypertension, Hannover Medical School, Hannover, Germany.
Cell Death Discov. 2023 Oct 25;9(1):395. doi: 10.1038/s41420-023-01686-6.
The complement system is a part of the innate immune system in the fluid phase and efficiently eliminates pathogens. However, its activation requires tight regulation on the host cell surface in order not to compromise cellular viability. Previously, we showed that loss of placental cell surface sialylation in mice in vivo leads to a maternal complement attack at the fetal-maternal interface, ultimately resulting in loss of pregnancy. To gain insight into the regulatory function of sialylation in complement activation, we here generated trophoblast stem cells (TSC) devoid of sialylation, which also revealed complement sensitivity and cell death in vitro. Glycolipid-analysis by multiplexed capillary gel electrophoresis coupled to laser-induced fluorescence detection (xCGE-LIF) allowed us to identify the monosialoganglioside GM1a as a key element of cell surface complement regulation. Exogenously administered GM1a integrated into the plasma membrane of trophoblasts, substantially increased binding of complement factor H (FH) and was sufficient to protect the cells from complement attack and cell death. GM1a treatment also rescued human endothelial cells and erythrocytes from complement attack in a concentration dependent manner. Furthermore, GM1a significantly reduced complement mediated hemolysis of erythrocytes from a patient with Paroxysmal nocturnal hemoglobinuria (PNH). This study demonstrates the complement regulatory potential of exogenously administered gangliosides and paves the way for sialoglycotherapeutics as a novel substance class for membrane-targeted complement regulators.
补体系统是液相中固有免疫系统的一部分,可有效清除病原体。然而,其激活需要在宿主细胞表面进行严格调控,以免损害细胞活力。此前,我们发现小鼠体内胎盘细胞表面唾液酸化缺失会导致母胎界面处母体补体攻击,最终导致妊娠失败。为深入了解唾液酸化在补体激活中的调节功能,我们在此生成了缺乏唾液酸化的滋养层干细胞(TSC),这也揭示了其在体外对补体的敏感性和细胞死亡。通过多重毛细管凝胶电泳结合激光诱导荧光检测(xCGE-LIF)进行糖脂分析,使我们能够确定单唾液酸神经节苷脂GM1a是细胞表面补体调节的关键元素。外源性给予的GM1a整合到滋养层细胞膜中,显著增加了补体因子H(FH)的结合,并足以保护细胞免受补体攻击和细胞死亡。GM1a处理还以浓度依赖的方式拯救了人类内皮细胞和红细胞免受补体攻击。此外,GM1a显著降低了阵发性夜间血红蛋白尿(PNH)患者红细胞的补体介导的溶血。这项研究证明了外源性给予神经节苷脂的补体调节潜力,并为唾液糖疗法作为一种新型的膜靶向补体调节剂物质类别铺平了道路。