Where do the depleted plasma amino acids go in phenylketonuria?
作者信息
Christensen H N
出版信息
Biochem J. 1986 Jun 15;236(3):929-30. doi: 10.1042/bj2360929.
Abstract
摘要
相似文献
1
Where do the depleted plasma amino acids go in phenylketonuria?苯丙酮尿症中消耗的血浆氨基酸去向何处？
Biochem J. 1986 Jun 15;236(3):929-30. doi: 10.1042/bj2360929.
2
Hypothesis: where the depleted plasma amino acids go in phenylketonuria, and why.假设：苯丙酮尿症中消耗的血浆氨基酸去向何处以及原因。
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Evaluation of trace element and mineral status and related to levels of amino acid in children with phenylketonuria.苯丙酮尿症患儿微量元素和矿物质状况及其与氨基酸水平的关系评估
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Glutamine depletion in phenylketonuria. A possible cause of the mental defect.
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Reduction of large neutral amino acid concentrations in plasma and CSF of patients with maple syrup urine disease during crises.枫糖尿症患者发作期血浆和脑脊液中大量中性氨基酸浓度的降低。
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Evidence for inhibition of exodus of small neutral amino acids from non-brain tissues in hyperphenylalaninaemic rats.高苯丙氨酸血症大鼠非脑组织中小中性氨基酸外流受抑制的证据。
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本文引用的文献
1
[On the pathogenesis of feeble-mindedness in phenylketonuria].
Klin Wochenschr. 1962 Mar 1;40:225-6. doi: 10.1007/BF01477102.
2
DISTINCT MEDIATING SYSTEMS FOR THE TRANSPORT OF NEUTRAL AMINO ACIDS BY THE EHRLICH CELL.艾氏细胞转运中性氨基酸的不同介导系统。
J Biol Chem. 1963 Nov;238:3686-99.
3
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Intensified gradients for endogenous amino acid substrates for transport system L on injecting a specific competitor for that system.
Life Sci. 1981 Aug 17;29(7):749-53. doi: 10.1016/0024-3205(81)90029-1.
6
Disturbances of amino acid transport in rats with experimental hyperphenylalaninaemia.实验性高苯丙氨酸血症大鼠氨基酸转运的紊乱
J Inherit Metab Dis. 1981;4(2):105-6. doi: 10.1007/BF02263613.
7
Effect of elevated plasma phenylalanine levels on other amino acids in phenylketonuric and normal subjects.血浆苯丙氨酸水平升高对苯丙酮尿症患者和正常人其他氨基酸的影响。
J Pediatr. 1969 Mar;74(3):399-405. doi: 10.1016/s0022-3476(69)80197-6.
8
Effects of non-metabolizable analogs on the distribution of amino acids in the rat.不可代谢类似物对大鼠氨基酸分布的影响。
Biochim Biophys Acta. 1968 Mar 1;150(2):237-52. doi: 10.1016/0005-2736(68)90167-3.
9
The influence of high phenylalanine and tyrosine on the concentrations of essential amino acids in brain.高苯丙氨酸和酪氨酸对脑中必需氨基酸浓度的影响。
J Neurochem. 1968 Mar;15(3):235-41. doi: 10.1111/j.1471-4159.1968.tb06202.x.
10
Effect of amino acids and proteins on insulin secretion in man.
Recent Prog Horm Res. 1967;23:617-62. doi: 10.1016/b978-1-4831-9826-2.50017-9.
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