Department of Ultrasonography, Affiliated Jinhua Hospital, Zhejiang University School of Medicine, Jinhua city, China.
Department of Urology, Affiliated Jinhua Hospital, Zhejiang University School of Medicine, Jinhua city, China.
J Int Med Res. 2023 Oct;51(10):3000605231207756. doi: 10.1177/03000605231207756.
An aortico-left ventricular tunnel is a rare congenital heart disease, and its prenatal diagnosis is even rarer. This report describes a fetus diagnosed with an aortico-left ventricular tunnel at 26 weeks of gestation. After delivery, the infant exhibited cyanosis and cessation of breathing. After resuscitation, he was transferred to the neonatal intensive care unit. Echocardiography confirmed an aortico-left ventricular tunnel. The infant survived after surgical repair. An aortico-left ventricular tunnel can be diagnosed by antenatal ultrasound, and prompt neonatal management can help to prevent perinatal morbidity and mortality.
主动脉-左心室隧道是一种罕见的先天性心脏病,其产前诊断更为罕见。本报告描述了一例在 26 孕周时被诊断为主动脉-左心室隧道的胎儿。出生后,患儿出现发绀和呼吸停止。复苏后,患儿转入新生儿重症监护病房。超声心动图证实存在主动脉-左心室隧道。患儿经手术修复后存活。产前超声可诊断主动脉-左心室隧道,及时的新生儿管理有助于预防围产期发病率和死亡率。