Abseyi Sema Nilay, Şıklar Zeynep, Özsu Elif, Kayı Cangır Ayten, Cabi Ünal Emel, Taçyıldız Nurdan, Aycan Zehra, Berberoğlu Merih
Ankara University Faculty of Medicine, Department of Pediatric Endocrinology, Ankara, Türkiye
Ankara University Faculty of Medicine, Department of Thoracic Surgery, Ankara, Türkiye
J Clin Res Pediatr Endocrinol. 2025 Aug 22;17(3):352-358. doi: 10.4274/jcrpe.galenos.2023.2023-7-6. Epub 2023 Nov 9.
We report an adolescent boy diagnosed with ectopic adrenocorticotropin hormone syndrome (EAS) due to an atypical bronchial carcinoid. The patient was managed by a multidisciplinary team. He underwent surgery and subsequent chemotherapy and radiotherapy treatments. The patient is still under our follow-up. At the time of writing, eighteen pediatric and adolescent patients with EAS because of bronchial carcinoid tumors have been reported. EAS due to bronchial carcinoids is very rare in children and adolescents. Careful diagnostic evaluation and rapid treatment should be started immediately. Although complete remission is possible, atypical carcinoids have a more aggressive nature. A multidisciplinary approach and follow-up is recommended in terms of quality of life and survival.
我们报告了一名因非典型支气管类癌而被诊断为异位促肾上腺皮质激素综合征（EAS）的青春期男孩。该患者由多学科团队进行管理。他接受了手术以及后续的化疗和放疗。患者仍在我们的随访中。在撰写本文时，已有18例因支气管类癌肿瘤导致EAS的儿科和青少年患者被报道。支气管类癌导致的EAS在儿童和青少年中非常罕见。应立即开始仔细的诊断评估和快速治疗。尽管完全缓解是可能的，但非典型类癌具有更强的侵袭性。就生活质量和生存率而言，建议采用多学科方法并进行随访。
