Foundation for Prader-Willi Research, Covina, CA, USA.
Department of Rehabilitation Medicine, University of Washington, Seattle, WA, USA.
Sci Rep. 2023 Nov 23;13(1):20573. doi: 10.1038/s41598-023-48024-5.
The Hyperphagia Questionnaire for Clinical Trials (HQ-CT) is an observer-reported outcome measure that has been widely used in interventional studies to assess changes in hyperphagic behaviors in individuals with Prader-Willi syndrome (PWS). However, HQ-CT scores in the wider PWS population and the general population have not been reported. Here we report HQ-CT scores from more than 400 individuals with PWS and 600 typical individuals, aged 5-26. Overall, HQ-CT scores were significantly higher in those with PWS compared to typically developing individuals at all ages evaluated. In addition, while HQ-CT scores in the typically developing population decreased with age, scores increased with age in PWS. To further understand the variability of HQ-CT scores in the PWS population, semi-structured interviews were conducted with caregivers of a small subset of adults with PWS who had unexpectedly low HQ-CT scores. These caregivers reported that strict adherence to a food routine, food security measures and supervised food preparation reduced the frequency and intensity of hyperphagic behaviors measured by HQ-CT. Thus, hyperphagic behaviors are captured by the HQ-CT for most individuals with PWS, but for some individuals residing in settings with highly structured food routines, HQ-CT scores may not fully reflect the extent of PWS-associated hyperphagia.
《临床试验暴食问卷 (HQ-CT)》是一种观察者报告的结局测量工具,已被广泛用于干预性研究中,以评估普瑞德-威利综合征 (PWS) 个体暴食行为的变化。然而,HQ-CT 评分在更广泛的 PWS 人群和普通人群中的情况尚未报道。在此,我们报告了来自 400 多名 PWS 患者和 600 名典型个体的 HQ-CT 评分,年龄为 5-26 岁。总体而言,在所有评估的年龄中,PWS 患者的 HQ-CT 评分明显高于典型发育个体。此外,虽然典型发育人群的 HQ-CT 评分随年龄而降低,但 PWS 患者的评分随年龄而增加。为了进一步了解 PWS 人群中 HQ-CT 评分的可变性,我们对一小部分 HQ-CT 评分意外较低的成年 PWS 患者的照顾者进行了半结构化访谈。这些照顾者报告说,严格遵守饮食常规、食品安全措施和监督食物准备可以减少 HQ-CT 测量的暴食行为的频率和强度。因此,对于大多数 PWS 患者来说,暴食行为可以通过 HQ-CT 来捕捉,但对于一些居住在饮食常规高度结构化环境中的患者,HQ-CT 评分可能无法完全反映 PWS 相关的暴食程度。