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胆道闭锁与后颅窝出血:巧合还是因果关系。一例病例报告及文献综述

Biliary atresia and posterior fossa bleed: Chance or causality. A case report and review of the literature.

作者信息

Karki Susmin, Chand Vikash, Parajuli Asmita, Shilpakar Sushil Kumar, Regmi Prakash, Bhusal Kabi Raj

机构信息

Maharajgunj Medical Campus Tribhuvan University Institute of Medicine Kathmandu Nepal.

Department of Neurosurgery Tribhuvan University Institute of Medicine Kathmandu Nepal.

出版信息

Clin Case Rep. 2023 Nov 25;11(11):e8249. doi: 10.1002/ccr3.8249. eCollection 2023 Nov.

Abstract

KEY CLINICAL MESSAGE

A newborn with a rare form of biliary atresia had posterior fossa bleed and subarachnoid hemorrhage despite vitamin K prophylaxis, indicating biliary atresia is a causality rather than chance.

ABSTRACT

Biliary atresia frequently causes surgical jaundice, resulting in delayed vitamin K deficiency. We report a 28-day-old newborn diagnosed with a rare form of biliary atresia presented with an unusual association of posterior fossa bleed and subarachnoid hemorrhage despite vitamin K prophylaxis. Thus, biliary atresia remains causality rather than chance.

摘要

关键临床信息

一名患有罕见形式胆道闭锁的新生儿,尽管接受了维生素K预防治疗,仍出现后颅窝出血和蛛网膜下腔出血,提示胆道闭锁是病因而非巧合。

摘要

胆道闭锁常导致外科性黄疸,进而导致维生素K缺乏延迟出现。我们报告一例28日龄新生儿,诊断为罕见形式的胆道闭锁,尽管接受了维生素K预防治疗,仍出现了后颅窝出血和蛛网膜下腔出血这一不寻常的关联。因此,胆道闭锁仍是病因而非巧合。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/72a1/10675080/5623448e50ff/CCR3-11-e8249-g004.jpg

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