Cardiac Section, National Heart and Lung Institute (NHLI), Faculty of Medicine, Imperial College London, Hammersmith Campus, Du Cane Road, London W12 0NN, UK.
Department of Surgery, Dentistry, Pediatrics and Gynecology, Cardiovascular Science, The University of Verona, 37134 Verona, Italy.
Cells. 2023 Dec 4;12(23):2764. doi: 10.3390/cells12232764.
(1) Pulmonary hypertension (PH)-associated right ventricular (RV) failure is linked to a reduction in pulmonary vasodilators. Treprostinil has shown effectiveness in PAH patients with cardiac decompensation, hinting at potential cardiac benefits. We investigated treprostinil's synergy with isoprenaline in RV and LV cardiomyocytes. We hypothesised that disease-related RV structural changes in cardiomyocytes would reduce contractile responses and cAMP/PKA signalling activity. (2) We induced PH in male Sprague Dawley rats using monocrotaline and isolated their ventricular cardiomyocytes. The effect of in vitro treprostinil and isoprenaline stimulation on contraction was assessed. FRET microscopy was used to study PKA activity associated with treprostinil stimulation in AKAR3-NES FRET-based biosensor-expressing cells. (3) RV cells exhibited maladaptive remodelling with hypertrophy, impaired contractility, and calcium transients compared to control and LV cardiomyocytes. Combining treprostinil and isoprenaline failed to enhance inotropy in PH RV cardiomyocytes. PH RV cardiomyocytes displayed an aberrant contractile behaviour, which the combination treatment could not rectify. Finally, we observed decreased PKA activity in treprostinil-treated PH RV cardiomyocytes. (4) PH-associated RV cardiomyocyte remodelling reduced treprostinil sensitivity, inotropic support, and impaired relaxation. Overall, this study highlights the complexity of RV dysfunction in advanced PH and suggests the need for alternative therapeutic strategies.
(1)肺动脉高压(PH)相关的右心室(RV)衰竭与肺血管扩张剂的减少有关。曲前列尼尔在伴有心脏失代偿的 PAH 患者中显示出有效性,提示其可能对心脏有益。我们研究了曲前列尼尔与异丙肾上腺素在 RV 和 LV 心肌细胞中的协同作用。我们假设疾病相关的 RV 结构变化会降低心肌细胞的收缩反应和 cAMP/PKA 信号转导活性。(2)我们使用单硝酸异山梨酯在雄性 Sprague Dawley 大鼠中诱导 PH,并分离其心室心肌细胞。评估了体外曲前列尼尔和异丙肾上腺素刺激对收缩的影响。使用 FRET 显微镜研究了 AKAR3-NES FRET 基生物传感器表达细胞中与曲前列尼尔刺激相关的 PKA 活性。(3)与对照和 LV 心肌细胞相比,RV 细胞表现出适应性重塑,包括肥大、收缩功能受损和钙瞬变。在 PH RV 心肌细胞中,联合使用曲前列尼尔和异丙肾上腺素不能增强正性肌力。PH RV 心肌细胞表现出异常的收缩行为,联合治疗无法纠正。最后,我们观察到曲前列尼尔处理的 PH RV 心肌细胞中 PKA 活性降低。(4)PH 相关的 RV 心肌细胞重塑降低了曲前列尼尔的敏感性、正性肌力支持和舒张功能障碍。总的来说,这项研究强调了晚期 PH 中 RV 功能障碍的复杂性,并提示需要替代治疗策略。