Shankar Ruthwik B, Amberker Adheep B, Belgundi Vidyasagar
Pulmonary Medicine, JJM (Jagadguru Jayadeva Murugarajendra) Medical College, Davanagere, IND.
Cureus. 2023 Dec 1;15(12):e49769. doi: 10.7759/cureus.49769. eCollection 2023 Dec.
Morgagni hernia is a rare congenital defect of the diaphragm, especially seen in children but rarely observed in adults. It occurs due to a congenital defect during the development of the diaphragm. Bochdalek hernia is a common congenital form of diaphragmatic hernia. Morgagni hernia is usually rare with a prevalence of approximately 2-3%. Beaver tail liver, which is also called sliver of liver, is a rare variant of liver morphology. Sometimes elongated left lobe of the liver can extend laterally across the midline to contact and often surround the spleen. A 46-year-old female from Karnataka complained of fever with chills and lower back aches for seven days with no history of chest pain, vomiting, or diarrhea. There have been no similar complaints in the past. She had no other comorbidities. She was a non-smoker and non-alcoholic. Biomass gas exposure for 20 years was noted as she cooked food with firewood. She was a housewife by occupation with no history of trauma or surgeries in the past. The general physical exam was unremarkable. The respiratory system was normal. Auscultation showed decreased breath sounds in the mammary area of the right side of the chest with normal vesicular breath sounds in all other areas. Per abdominal exam showed a flat abdomen. Umbilicus was central in position. There was tenderness in the right hypochondriac and epigastric regions with no guarding or rigidity. On examining the cardiovascular system, apical impulses could not be palpated and normal heart sounds were heard with no cardiac murmurs. Other systems examination was normal. Routine blood investigations were done, revealing hemoglobin of 11.6%, total WBC of 6270 cells, and hematocrit of 33.1%. The renal function test was within normal limits (creatinine = 0.7 mg/dl). A chest X-ray revealed a right lower zone, para cardiac well-circumscribed structure suggestive of a cyst with an air-fluid level inside. Chest CT was suggestive of a hernia in the anterior aspect of the diaphragm measuring 3.5 x 3.3 cm at the level of D9 vertebral body with transverse colon and omentum as its contents, ascending upwards into anterior and superior mediastinum for a length of 13 cm causing shift of cardia posteriorly and to the left (anterior midline diaphragmatic hernia - Morgagni hernia). A hyperdense lesion (Hounsfield unit = 64) measuring 1.3 x 1.8 cm was noted in segment seven of the right lobe of the liver, suggestive of a complex cyst. Beaver tail was noted in the liver. Morgagni hernia usually presents in younger age groups with respiratory symptoms. Its incidental detection in adults is very rare. In this case, the patient was having lower backache and no other gastrointestinal symptoms. The respiratory and cardiothoracic systems get affected because the intestinal contents herniating through the diaphragm shift the position of the cardia and the lower lobes of the lungs, which may have implications such as repeated cough and infections. Symptomatic hernias are usually detected in an early age group. It can present with symptoms of gastrointestinal obstruction or acute chest symptoms or can even be asymptomatic. Treatment is primarily surgical repair of the hernia. This can be done either transthoracically or transabdominally. It is usually advised that surgical repair should be done even in asymptomatic cases as in this case, to avoid obstruction of the intestine or worsening of the hernia that is pulling the abdominal contents into the thorax.
莫尔加尼疝是一种罕见的先天性膈肌缺损,多见于儿童,成人中罕见。它是由于膈肌发育过程中的先天性缺陷所致。博赫达勒克疝是一种常见的先天性膈疝形式。莫尔加尼疝通常很罕见,患病率约为2%-3%。海狸尾状肝,也称为肝薄片,是一种罕见的肝脏形态变异。有时肝脏左叶拉长可横向越过中线,接触并常包绕脾脏。一名来自卡纳塔克邦的46岁女性主诉发热、寒战及下背部疼痛7天,无胸痛、呕吐或腹泻病史。既往无类似主诉。她无其他合并症。她不吸烟、不饮酒。据记录,她用柴火做饭有20年生物质气暴露史。她职业为家庭主妇,既往无外伤或手术史。全身体格检查无异常。呼吸系统正常。听诊示右侧胸部乳房区域呼吸音减弱,其他区域肺泡呼吸音正常。腹部检查示腹部平坦。脐位于中央。右季肋区和上腹部有压痛,无肌紧张或强直。检查心血管系统时,未触及心尖搏动,心音正常,无心脏杂音。其他系统检查正常。进行了常规血液检查,结果显示血红蛋白为11.6%,白细胞总数为6270个/立方毫米,血细胞比容为33.1%。肾功能检查在正常范围内(肌酐=0.7毫克/分升)。胸部X线显示右下区、心旁有边界清晰的结构,提示为一含气液平面的囊肿。胸部CT提示在第9椎体水平膈肌前部有一疝,大小为3.5×3.3厘米,内容物为横结肠和大网膜,向上延伸至前纵隔和上纵隔,长度为13厘米,导致贲门向后向左移位(前正中膈肌疝 - 莫尔加尼疝)。在右叶第7段发现一个高密度病变(亨氏单位=64),大小为1.3×1.8厘米,提示为复杂性囊肿。肝脏可见海狸尾状改变。莫尔加尼疝通常在较年轻年龄组出现并伴有呼吸系统症状。在成人中偶然发现非常罕见。在本病例中,患者有下背部疼痛,无其他胃肠道症状。呼吸和心胸系统会受到影响,因为通过膈肌突出到胸腔的肠内容物会改变贲门和肺下叶的位置,这可能导致反复咳嗽和感染等情况。有症状的疝通常在较早年龄组被发现。它可表现为胃肠道梗阻症状或急性胸部症状,甚至可能无症状。治疗主要是手术修复疝。可经胸或经腹进行。通常建议即使是无症状的病例,如本病例,也应进行手术修复,以避免肠梗阻或疝加重,将腹腔内容物拉入胸腔。