Saqib Sabah Uddin, Hamid Kulsoom, Chawla Tabish Umer
Aga Khan University Hospital, Karachi, Pakistan.
Int J Surg Case Rep. 2020;76:390-393. doi: 10.1016/j.ijscr.2020.10.021. Epub 2020 Oct 9.
Congenital Diaphragmatic hernia (CDH) is a condition in which there is a defect in the diaphragm present at the time of birth. Morgagni hernia is one of the two most common types of CDH which constitutes 2%-4% of diaphragmatic hernias. They mostly remain silent or discovered as an incidental finding on radiological studies. Symptomatic adult Morgagni hernias are extremely rare.
Elderly woman presented with a 1-day history of abdominal pain, vomiting, and acute onset of respiratory distress. There was no history of trauma to the chest or abdomen. After initial resuscitation, a Chest x-ray was performed which showed bowel shadow under the right hemidiaphragm. She then underwent computed tomography (CT), which showed a defect in the right hemidiaphragm and segment of herniated small bowel loop with fecalization into the thoracic cavity. After initial resuscitation, she underwent laparotomy, reduction of bowel loops, and primary repair of the hernia defect. Postoperatively she remained well and was discharged on 4th post-operative day.
Congenital diaphragmatic hernia occurs in 1 out of every 4000-5000 live births. A majority of the patients will be diagnosed either antenatally or will present with respiratory distress in the neonatal period. Presentation in adults is extremely rare and mostly characterized by abdominal pain, vomiting, intestinal obstruction with some acute respiratory distress, at the background of insignificant past medical history. Surgical management is the mainstay of treatment in symptomatic cases.
CDH of Morgagni type can present uncommonly in adults with symptoms. A good history and clinical examination along with aid of chest x-ray and CT scan should establish the diagnosis. Early surgical intervention is key to prevent ischemia and later gangrene of intestinal content.
先天性膈疝(CDH)是一种出生时膈肌存在缺陷的疾病。莫尔加尼疝是最常见的两种CDH类型之一,占膈疝的2%-4%。它们大多没有症状,或在影像学检查时偶然发现。有症状的成人莫尔加尼疝极为罕见。
一位老年女性,有1天的腹痛、呕吐病史,急性呼吸窘迫起病。无胸部或腹部外伤史。初步复苏后,进行了胸部X线检查,显示右半膈肌下方有肠影。随后她接受了计算机断层扫描(CT),显示右半膈肌有缺损,一段小肠袢疝入胸腔并出现粪样改变。初步复苏后,她接受了剖腹手术,回纳肠袢,并对疝缺损进行一期修复。术后她恢复良好,术后第4天出院。
先天性膈疝在每4000-5000例活产中出现1例。大多数患者将在产前被诊断,或在新生儿期出现呼吸窘迫。在成人中出现极为罕见,主要表现为腹痛、呕吐、肠梗阻,并伴有一些急性呼吸窘迫,既往病史不明显。手术治疗是有症状病例的主要治疗方法。
莫尔加尼型CDH在成人中可能以不常见的症状出现。详细的病史、临床检查以及胸部X线和CT扫描有助于确诊。早期手术干预是预防肠内容物缺血及随后坏疽的关键。